id	author	title	date	pages	extension	mime	words	sentences	flesch	summary	cache	txt
cord-297222-2danzbqt	Quadri, Syed P	An Intriguing Presentation of Epstein-Barr Virus-Associated Hemophagocytic Lymphohistiocytosis	2020-08-05		.txt	text/plain	2094	125	37	Hemophagocytic lymphohistiocytosis (HLH) is an immune related clinical syndrome with protean manifestations, varying presentation, clinically complex, with diverse causes, and is an under-recognized entity which carries high morbidity and mortality. Hemophagocytic lymphohistiocytosis (HLH) is an extremely rare and potentially lifethreatening hematological disorder, characterized by clinical features of extreme inflammation and an unregulated immune system. We describe a case of Epstein-Barr virus (EBV)-associated HLH with its typical diagnostic challenges and associated high mortality rate, but an early prompt diagnosis with appropriate treatment can lead to better outcomes. The major finding in the patient's autopsy was hemophagocytic histiocytosis with rare EBVpositivity noted in the bone marrow analysis, suggesting that the HLH was due to EBV infection. The official cause of death in the patient was determined to be pulmonary aspergillosis with organizing pneumonia in the setting of hemophagocytic lymphohistiocytosis, likely secondary to Epstein-Barr virus infection.	./cache/cord-297222-2danzbqt.txt	./txt/cord-297222-2danzbqt.txt