[PDF] Maple syrup urine disease hair reveals the importance of 18-methyleicosanoic acid in cuticular delamination. | Semantic Scholar Skip to search formSkip to main content> Semantic Scholar's Logo Search Sign InCreate Free Account You are currently offline. Some features of the site may not work correctly. DOI:10.1016/J.MICRON.2004.11.004 Corpus ID: 25312301Maple syrup urine disease hair reveals the importance of 18-methyleicosanoic acid in cuticular delamination. @article{Smith2005MapleSU, title={Maple syrup urine disease hair reveals the importance of 18-methyleicosanoic acid in cuticular delamination.}, author={J. Smith and J. A. Swift}, journal={Micron}, year={2005}, volume={36 3}, pages={ 261-6 } } J. Smith, J. A. Swift Published 2005 Chemistry, Medicine Micron 18-Methyleicosanoic acid (18-MEA) is thought to be covalently bound to the outer surface of human hair and is a major component of the outer beta-layer of the cuticular cell membrane complex (CCMC). Cuticular delamination, whether this occurs between the outer beta- and delta-layers or within the plane of the beta-layer, results in a fresh layer of 18-MEA being exposed at the newly-revealed surface. Hair from patients with Maple Syrup Urine Disease (MSUD), however, does not contain 18-MEA and… Expand View on PubMed researchportal.port.ac.uk Save to Library Create Alert Cite Launch Research Feed Share This Paper 13 CitationsBackground Citations 2 View All Figures and Topics from this paper figure 1 figure 2 figure 3 figure 4 figure 5 figure 6 View All 6 Figures & Tables Maple Syrup Urine Disease 18-methyleicosanoic acid Transmission Electron Microscopy Scanning Electron Microscopy anatomical layer negative regulation of border follicle cell delamination Microscopy, Atomic Force Keto Acids Iridium Thioctic Acid Hair Cuticular layer of tympanic membrane Twins, Conjoined 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) Plasma membrane Syrup Drug Form Acer Cuticle One Thousand alpha-Mannosidosis 13 Citations Citation Type Citation Type All Types Cites Results Cites Methods Cites Background Has PDF Publication Type Author More Filters More Filters Filters Sort by Relevance Sort by Most Influenced Papers Sort by Citation Count Sort by Recency Lipid distribution and influence on hair structure M. 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Matsuo Biology, Medicine Molecular genetics and metabolism 2004 20 View 2 excerpts, references background Save Alert Research Feed Microscopical investigations on the epicuticle of mammalian keratin fibres J. A. Swift, Joshua R. Smith Biology, Medicine Journal of microscopy 2001 61 View 1 excerpt, references methods Save Alert Research Feed Cleavage of Integral Surface Lipids of Wool by Aminolysis D. Evans, Miklos Lanczki Chemistry 1997 48 View 2 excerpts, references background Save Alert Research Feed ... 1 2 3 ... Related Papers Abstract Figures and Topics 13 Citations 27 References Related Papers Stay Connected With Semantic Scholar Sign Up About Semantic Scholar Semantic Scholar is a free, AI-powered research tool for scientific literature, based at the Allen Institute for AI. 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