-- BM University of California San Di«gO. 1 - -^ -^OJEGO- III — 'I I BIO' HY UNIVERSIT SAN DIEGO DATE DUE lyyiiii -SE^ 1 \ nrr"n 1 ^'^CT P^.e Recini read 01. Ricini. 168. The twenty first line from the bottom, for Iriaugular read triangular. 175. The ninth line from the top, for mdeoraie read mnderate. 191. The eighteenth line from the top, for Jnuraal read Journal. 202. The top line, for cases which read cases in which. 335. The eighth line from the bottom, for dilate read dilute. Explanation of plate third. The second line from the top, for Case X/7/read Case XJ^VII. EXPLANATION OF THE PLATES. PLATE II. Some of the Instruments employed in Proctoplasty, Colotomy, &c. Figure 1, Figure 2. Figure 3. Figure 4. Figure 5. Figure G. Figure 7. Figure 8. Figure 9. Figure 10. Figure 11. Figure 12. EXPLANATION. Small Bi-valve Speculum Ani. Operating Scalpel of medium size. Small size Scalpel for delicate work. Probe-pointed curved Bistoury. Cooper's Hernial Bistoury. Gurved Sharp-pointed Bistoury. Straight Sharp-pointed Bistoury. Flexible-Silver grooved Director. Bull-dog Forceps of Listen, for pulling down the end of the rectum. Tumor Forceps, for drawing down the blind end of the rectmn. Round-bellied Scalpel, for making the first incision of the perinasum. Silver Anal Canula, Plar.p 11 PLATE III. Plate III. represents a case of membranous occlusion of the Anus, as seen tij Von Amnion. [Vide Case XIII.] EXPLANATION. Figure 1, presents the external appearance of this case. After Von Amman, a — The penis in a constant state of erection. h — A. considerable pit or depression near the natural situation of the anus. Figure 2, presents the appearance of the intestines. After Von Ammon. a^ a, a. — The descending colon greatly distended with gas and meconium, just where it terminates in the rectum. h. — The small intestines turned over on the right side. Figure 3, presents the inferior portion of the rectum. After Von Ammon. a. — The rectum. h. — The place at which the anus was closed. c. — A sound in the orifice made by the operation. Figure 4, presents the rectum laid open through its entire length. After Von Ammon. a. — The inner surface of the rectum. h. — The folds of the rectum, or columns of Morgagni. c. — The internal sphincter, forming a wreath-like mass, from which the membrane grew which had closed the anus. cj^ (J, — The cut surfaces of the rectal walls greatly thickened. Plate 111. FlQ. /. J:' \ "/ ^ - / I PLATE lY. EXPLANATION. Figure 1, represents tlie external appearance of an imperforate anus and rectum, in a new-born infant. [Third Species.] a. — The prominent and continuous raphd. Figure 2, represents the parts immediately concerned in a case of imper- foration of the anus and rectum, as they were observed by Von Ammon in a five months' foetus. [Vide Case L.] After Von Ammon. ffl.— The rectum. h. — The cul-de-sac of the rectum. c. — The cord-like rudiment of the rectum. d. — The sigmoid flexure of the colon. Figure 3, gives a representation of the parts concerned in Dr. W. P Hill's case of imperforate anus and rectum. [Vide Case LXILJ a. — A portion of the perinfeum. t, h. — The ureters. e. — The rectum terminating upon the neck of the bladder, d.: — The urethra. «.. — The- bladder. Plate IV ife ^ PLATE V. Plate V. gives a full representation of the celebrated case of M. Amussat, and his peculiar operation. [Vide Case XLII.j EXPLANATION. Figure 1, is an imaginary representation of this case. M. Amussat, in order to render the details of his operation intelligiVjle, gave a plan of the parts a-s he supposed them to exist before the operation. He took pains to make the analogy as complete as possible, by taking his sketch from a left- side view of the interior of the pelvis, in a female child who died a few days after birth. All the organs of the pelvis had been cut in two, part of the rectum was removed, to represent the deficient portion of the intestine, and the anus was made to communicate with the vagina. After Boitrgery. a, h. — The anus and vulva, which were properly formed, and communi- cated with the vagina onl3^ c. — The extremity of the rectum forming a cul-de-sac below tne sacro- vertebral angle, and having no communication with either the anus or vagina. fZ.— The bladder. e. — The superior portion of the rectum. Figure 2, represents Amussat's operation in this case. After Bourgery. «, h. — The fingers of an assistant. c. — The sound introduced into the vagina. d. — The loop of a ligature. f. — The bistoury. Figure 3, represents the conclusion of this operation. The horizontal wound is closed by sutures, and the margins of the longitudinal wound are united to the divided portions of mucous membrane. After Bourgery, k-'^ I /r'> PLATE VI. EXPLANATION. Figure 1, represents a case -of complete imperforation of the rectnm, situated some distance above a normal anus. fFourtli Species.] After Baillie. a. — The rectum. h. — The cul-de-sac and termination of the rectum. c. — The normal anus. d. — A bougie introduced into the short anal canal, as far up as to the blind end of the rectum. e. — The anterior surface of the bladder. /. — The posterior surface of the bladder. g. — A part of one of the ureters. Figure 2, represents the part concerned in a case oNmperforation of the rectum above a normal anus, as observed by Mr. Ford. [Vide Case LXX.] a. — The rectum laid open through its entire length. b. — The ligamentous substance described by Mr. Ford. c. — The normal anus. d. — The place at which the rectum was occluded. Plate VI Fij. /. / w<. .i>«t»v 6' d PLATE VII. Plate YII. gives a representation of the rectum and part of the colon of a new-born infant, seen by Yon Amnion, in whom existed a membranous closure of the rectum three-fourtlis of an inch above a normal anus. The child was in a dj'ing state when Von Amnion was called, and no operation was performed. [Fourth Species.] {Op. Clt. Tah. X. Figs. 9, 10, 11.) EXPLANATION. Figure 1, presents a front view of the rectum, from the point of occlu- sion to its connection with the colon. After Von Ammon. a. — The rectum greatlj' distended. /;. — The cul-de-sac of the rectum and point of occlusion. c. — The sigmoid flexure of the colon. (J.— The bladder. Figure 2, gives a lateral view of the rectum in the same case. After Von Ammon. a. — The large sack-like rectum. b. — The point of occlusion of the rectum. r. — The circular fibres of the external sphincter. L — The normal anus. e. — The bladder, small and contracted. /. — The urethra. g. — The sigmoid flexure of the colon. Figure 3, represents the inferior portion of the rectum laid open from the verge of the anus to the occluding membrane. After Von Ammon a. — The blind sac of the rectum. h. — The membranous closure of the rectum. i sl beautiful specimen, umbilical hernia, and a "preternatural anus. [Vide Case CXXXV.] After Von Ammon. a. — The ileum severed. ^.— The annulus umbilicalis. c. — The funiculus umbilcalis. d. — Hernia umbilicalis. e. — Vena umbilicalis. /• — The colon descending with a considerable curve and prolongation, to communicate with the bladder. 9, g. — The bilobed bladder. /t.— The termination of the prolonged colon in the bladder, between the ureters. i, i. — The ureters. j- — A probe in the preternatural anus. k. — The urethra severed. /, m. — The two vasa deferentia. Plate IX PLATE X. EXPLANATION. Figure 1, represents the very interesting case reported by Mr. Lucas, in which the rectum terminated in a cul-de-sac two inches above its natu- ral outlet, and communicated with the bladder. [Vide Case CXXXVI] After Mieban. a. — The rectum, terminating nearly two inches from the anal aperture. I). — The bladder. c. — A probe passed through a small opening by which the pouch-like termination of the rectum communicated with the bladder. d. — A probe passed from the anal aperture upwards, showing its deter- mination in the bladder ; the vesical oritice being guarded by a val- vular fold of mucous membrane. f, e, c. — A probe passed from the external orifice of the urethra aloug that tube into the bladder. /. — The distended portion of tho urethra, the diameter of which is equal to a No. li bougie. g. — The distended scrotum communicating with the urethra for fully half its length, and lined with a coating of lymph, which presented extravasation of the urine, and the liquid fasces into the cellular tissue. /;. — A small cul-de-sac corresponding to the urachus. Figure 2, represents the case reported by the late Dr. Steele, of Saratoga Springs, in which the rectum terminated in the neck of the bladder. [Vide Case CXXXIX.] a. — The rectum and r)art of the colon. 6.— The bladder. r. — The penis. Figure 3, represents an imaginary section of the pelvis, to explain the imperforation of the anus, and the urethra as they were supposed to exist in M. Roux de Brignole's case. ffl, a. — The interior of the bladder. h, h. — Section of the prostate. c. — The vesicula seminales. d. — The vas deferens. f, e. — The interior of the rectum.. /; — Supposed termination of the rectum in front of the neck of the bladder. g. — The penis. h. — The opening of the meatus. i. — The bulb of the urethra. k. — The root of the right corpus cavernosum. I. — Section of the pubis. ni. — Space between the pubis and the bladder. n, — The urachus. 0. — The muscles of the abdomen. p. — The skin. q, r. — The peritonaeum lining the cavity of the abdomen. >v, s. — The sacrum. /, t. —The incision in the perinseum. n. — The bistoury, its point in the rectum. P]Qr o Y PLATE XI. Plate XI. gives the representation of a remarkable foetus observed by M. Cruveilhier, in which the anus was imperforate, and the rectum termi- nated in the bladder. [Vide Case CXL.] EXPLANATION. Figure 1, represents the ano-perinseal region of this case. It will be observed that the perinseimi is enormous in its antero-posterior diameter. After Cruveilhier. Figure 2, represents a section of the pelvic cavity containing the soft parts. After Cruveilhier. a. — The bladder. h. — The rectum which opens into the bladder, and with the base of which is perfectly confounded. c, c. — The ureters. d. — The prostatic portion of the urethra. Figure 3, represents the rectum of this same case, opening into the posterior part of the bas-fond of the bladder by a large infundibuliform aperture. After Cruveilhier. a. — The rectum opening behind the bladder. h. — The prostatic portion of the urethra. c. — The infundibuliform aperture of the rectum communicating with the bladder. d. — The bladder laid open, showing its interior. PlnhnX Fifj. 1. ^^I^r ' itiy iS^g!*'"' Fii^ 3. jl PLATE XII. Plate XII. gives the representation of the case of a male child, present- ing an imperforation of the anus with the rectum terminating in the blad- der. It was seen by Von Amnion, and operated on without success. s EXPLANATION. Figure 1, gives the external appearance of this case. After Von Ammon. a, a. — The thighs slightly elevated. h. — A depression or pit in the exact situation of the absent anus. c. — The scrotum. d. — Another depression corresponding with the termination of the rec- tum within. Figure 2, represents a side view of the internal parts directly concernec iu this case. After Von Ammon «.— The bladder. h. — The inferior extremity of the colon. c. —The rectum adhering to and terminating in the posterior part of tht bladder between the insertion of the ureters. d, d. — The ureters. e,f. — The remaining portion of the integument and cellular tissue of tht perinajum not cut away. g. — The place where the depression was, and into which the bistour;y was plunged. Figure 3, presents another view of the relation existing between tin several internal parts of this case. After Von Avimov. ffl. — The bladder, presenting its posterior aspect. h, h. — The ureters, the right one presenting a remarkable turn in it. c, c. — The kidneys. d. — The portion of the perinseum not removed, in which the depression was at the normal situation of the anus. e. — The rectum laid open and its cavity exposed, so that the ojifice com- municating with the bladder is distinctly seen. /. — The recto-vesical orifice between the ureters. V n \' FL(f. I. I PLATE XIII. EXPLANATION. Figure 1, represents the case reported by Fleischmann, in which the anus and the rectum were entirely wanting, and the colon terminated in a blind sac. The abdomen is opened and its parietes turned over, tha^ aflfording a correct view of the situation of the intestines, especially show- ing the character of the descending colon. [Vide Case CCLIV.] After Von Amman. a. — The liver above the commencement of the ascending colon. b. — The ascending colon which here takes place of the caecum, and is divided into two branches, from one of which springs the appendi- cula vermiformis. c. — The descending colon, hanging loosely in the abdominal cavity. d. — The blind end of the colon, e, e, e, e. — The parietes of the abdomen. Figure 2, represents the anatomical condition of the colon in a case of imperforation of the anus and rectum, as observed by Von Ammon. The descending colon presents several sac-like dilations before passing down behind the bladder to terminate in a cul-de-sac in the rectum. After Von Ammon. a. — The descending colon. 6, &. — The sac-like dilations of the colon. c. — The bladder, behind which the colon passes. d, e.— The small intestines in a normal condition. PlateX Fi-vi . I Fiq. 2. PLATE XIV. Plate XTV. gives a representation of the case of a male child presenting an imperforation of the anus and rectum, unsuccessful!}- operated on by Von Amnion. The autopsy in this interesting case clearly revealed the cause of the failure of the operation. l"he rectum for about two-thirds of its entire length was greatly dilated, presenting the form of a pouch ; but gradually tapered off, and terminated blindly in a small point within a few lines of the posterior wall of the scrotum. Notwithstanding the incision was made in the proper place, and deep enough, yet it entirely failed to reach the rectum, because this organ was further removed from the sacrum towards the front than the natural, and thus occupying an abnormal position. [Vide page 102.] Had this fact been previously known to Von Amnion, and his incision directed much more towards the inter-pubic space than towards the sacrum, the rectum would doubtless have been easily opened. (Opus Citatum, S. 48.) EXPLANATION. Figure 1, represents a front view of the pelvic region of this case. The scrotum and penis are much corrugated, and drawn closely to the abdo- men, the latter presenting a para-phimosis congenita. The right half of the scrotum is turgid, and contains the ttisticle, w^hilst the left half presents less turgesence, the testicle not having descended into it. After Von Ammon. «, a. — The interior parietes of the abdomen. b. — The symphysis of the pubis. c. - The scrotum. d. — The penis. f. — The right half of the scrotum. /', q. — The dilated rectum. //, /. — The colon with its sigmoid flexure much smaller in diameter than natural. Figure 2, represents a side view of a portion of the contents of the j)e]vis. After Von Ammon. a. — The rectum. '^- — 'f he rectum terminating blindly in a conical point beneath the penis. '■•. — The bladder opened from the side. d. — The urethra opened from the side, f- — The artificial orifice made at the normal situation of the anus. Figure 3, presents a po.-terior view of the contents of the pelvis. After Von Ammon. a, a. — Both halves of the scrotum. h. — A probe indicating the entrance and the direction of Von Ammon's incision behind the rectum, and between it and the sacrum, f, c. — The superior part of the rectum descending in the form of a cone in front of the incision. (■?, d. — The intestines, f, e. — The interior surface of the peritongeum. PlateXlV. Fuf. 1. PLATE XV. Plate XV. gives representations of the operation for the formation of abdominal artificial anus. EXPLANATION. Figure 1, presents a front view of the surgical relations of the colon. After Bernard and Huette. a^ a. — The integuments. h, h. — The external oblique muscle. c. — The internal oblique muscle. d. — The transversalis muscle. e. — The lower edge of the liver. /. — The distended caecum. g. — The descending colon with the sigmoid flexure seen below. h. — The transverse colon. Figure 2, presents a posterior view of the parts concerned, as shown by- removing the dorsal structures. After Bernard aud Huette. a. — The peritonaeum. It. — The kidney. c. — The mesentery. d. — The bowels. e. — The colon. /. — The spine. Figure 3, represents the operation of Littrd for the formation of an artificial anus at the right groin. After Bernard and Huette. a, a. — The outline of the colon. h, b. — The extent of inguinal incision in the integuments. c, c. — An instrument passed beneath the distended colon, in order to bring it to the front wound. d. — The point of the colon which is to be perforated. Figure 4, represents the shape and appearance of the anus formed by the operation of Littre'. The long diameter of the opening corresponds to the line of the groin, and the bowel is so attached to the edges of the in- cision in the abdomen as to prevent contraction of the orifice, or the escape of the bowel into the abdomen. After Bernard and Huette. Figure 5, represents the operation of Littre', as modified by Pillore. Section of the ca;cuni. After Bourgery. Figure 0, represents Pillore's operation for iliac artificial anus completed. The wound in the intestine united to the wound in the integument by six I <;ints of twisted suture. After Bourgrry. PlahnXV l'i(j . I . Fiq. Z d.. "iW^.'^^^* Fiuf 3 'A^^^^£-'^^^ Fia. '%%^ d: :% PLATE XVI. Plate XVI. illustrates Callisen's operation for abdominal artificial anus, as modified by Amussat. EXPLANATION. Figure 1, represents the operation of Amussat, for tlie formation of aa abdominal anus in the left lumbar region. After Bernard and Huetle. a. a. — The outlines of the descending colon. 6, 6. — The extent of the incision in the integuments. c, c. — An instrument placed beneath the bowel to render it prominent. d, d. — Ligatures passed through the bowel in order to attach it to the sides of the wound, before it is perforated. Figure 2, represents the appearance of the artificial anus formed in Amussat's operation, showing the position of the sutures and the character of the opening. After Bernard and Huette. Figure 3, represents the lumbar artificial anus established bj' Amussat. After Bonrgery. PlaLeXVl F"J ' .^^ia^^~ Fvg 3 Ftg. Z ON THE CONGENITAL MALFORMATIONS OF THE RECTUM AND ANUS. CH^I^TER I. INTKODUCTION. SECTION L BIBLIOGRAPHY. A. 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Dissertatio de preter natur ali et raro InUstini Recti cum Vesica Urinaria, Coaliiii., et indepen- dente Ani Defectu. Gottmgen : 1779. Also, Comrnenta- tionum Medici., Physiologici, Anatomici et Ohstetrici Ar- gumenti. p. 172. Tab. VII. Gotting. : 1800. Y. York (J. H.) Boston Medical and Surgical Journal. Vol. XLlIp.^n. Boston: V^h^. Z. Zacntiis (Lnsitanus.) Prax. Med. Admir. Libri III. observ. 72. SECTIOK II. GENERAL REMARKS. The rectum and its teriniiuil ap})aratus, the anus, like other portions of the organization, are liable to malformations and imperfections, the result of some extraordinary derangement of the acts of the plastic energies at some period during the evolution of the embryo or the foetus in utero. From the remotest antiquity the congenital closure of the anus or the rectum was noticed by the Greek, the Roman and the Arabic physicians. They however looked upon it gener- ally as beyond the power of art to remedy, and consequently as possessing no interest in their estimation beyond that of a lusus natui'CB. These congenital vices of structure have been designated by the terms — Lnperforate Alius. — English. Imperforatio. ] Atresia Ani, v Latin. Clausitra. ) Imperf oration De V Anus. \ -p, -j Impeiforation Du Rectum. \ Yerschliessung Des Mastdarmes. — German. There is however a manifest impropriety in the application of some of these terms to many of the malformations of these parts. Under the generic term — Imperforate A mis, malform- ations of the anus and the rectum are included which differ essentially from each other, with regard to situation, form, cause and result. It is therefore imj^roper to denominate a case imperforate anus, in which the anus itself is pervious, although otherwise malformed ; or in wliich the anus is per- fectly natural, the deformity or imperforation being in the rectum, more or less distant above the normal anus ; or in which there is an entire absence of the anus. Each one of [37] 38 INTKODUCTION. these terms is too exclusive in its signification to embrace all the malformations of these organs, or to be used as a generic term in relation to them, consequently not one of them can ever be so used with propriety. Some of these vices of conformation are by no means un- common, and all of tliem are in a practical point of view, more or less important. Many of them are remediable, and as they generally admit of no delay in their treatment, but demand prompt means for their relief, a knowledge of all the medical and surgical measures which experience has decided to be best adapted to remedy each particular deformity, is of the utmost importance to every surgeon and accoucheur. In the absence of such knowledge no practitioner in this respect is able to discharge his professional duties with satisfaction to the public, or with an easy conscience to himself. In these instances nothing can be expected from any efforts of nature towards eflecting any substantial relief. If no operation is undertaken, death must soon follow from necessity. Nothing will avail but some surgical interference, for Nature has not dealt with the human species as she has with some of the in- sect tribes, for instance the ant^ which according to the ob- servations of the great natural historian Keaumur, has neither an anus nor any intestinal excrements that can be perceived. {Memoire pour Vllist. des Insect, tome vi. Mem. 10.) No accoucheur should ever neglect the important duty of examining minutely every infant immediately after its birth, and for a day or two subsequently, to ascertain without a doubt that there is an anal aperture, that the canal for some distance above is pervious, and that the parts perform their normal functions. Tliis important duty is too often neglected by persons engaged in the practice of midwifery. Tliere is one thing, however, that is scarcely ever neglected, especially by female accoucheurs and monthly nurses, and that is the pernicious practice of thoroughly purging new-born infants, irrespective of circumstances. One of the pleas set up for INTKODUCTION. 39 admin isteriug the v;iri(»iis nauseating- clniuglits to which new- born children are subjected, is tlie great dread in southern climates of trismus nascentiwm / the popular and erroneous idea being that trismus is the necessary result of retained me- conium. This practice is especially pernicious in cases in which there is a permanent obstruction in the lower bowel from malformation. In such cases it is obvious that purgative medicine would prove not only useless, but highly injurious ; indeed physic or improper food either would only induce pa- roxysms of pain and vomiting, and hasten the fatal result. — Tlic little sufferer thus often falls a victim, either to ignorance or to a false philanthropy. It would be far better and much more humane to suffer such patients to die slowly of inani- tion, than to torture them to death rapidly by the free use of improper food or medicine. In hopeless cases, if absolute diet is enjoined, it is surprising how long the little patients will survive apparently with but little suffering before they succumb to the effects of inanition. Professor Dewees men- tions two cases in point, " Dr. Hallam delivered a patient of a fine muscular, fat and healthy child, which had an im- pervious oesophagus, so that no food ever passed into the sto- mach. The child lived thirteen days, but was so wasted that its skin hung like a loose garment, and could be lapped and folded over its limbs." In another instance says Dr. Dewees, " a child was born with every external appearance of healthy conformation, but upon attempting to give it a little molasses and water, it had nearly strangled. Upon looking into its mouth, it was discovered that there was no vault to it ; neither was there a vestige of soft pallet. It never swallowed a drop — ^indeed every attempt w^as followed with such terrible dis- tress by the fluid passing into the trachea, that the trial w^as abandoned. It lived ten days — became extremely emaciated and very yellow^" {A System of Midwifery^ p. 215. Phil. 1832.) Food, in all cases of obstruction of the anus or the rec- tum from malformation, should be very cautiously adminis- 40 INTRODUCTION. tered. or altogether proscribed, with the exception of the mo- ther's milk, or a little sugar and water, until the obstruction is removed ; and if this cannot be accomplished and death is inevitable, let this event take place gradually by inanition, rather than speedily by repletion. Purgative medicines in all such cases are entirely inadmissible ; although I am aware that some able surgeons advise them for the pui'pose of forc- ing down, if possible, the end of the rectum preparatory to searching for it. It is generally believed that the congenital malformations of these parts are quite unconmon. Mr. AVest says that " The affection (meaning imperforate anus) in any form is so rare as to render a correct estimate of the comparative frequency of its varieties by no means easy." {Lectures on the Diseases of L fancy and Childhood., Amei'ican Edit. p. ^74:. Phil. 185-t.) Mr. Collins says that he only observed one instance of it out of 16,645 children born in the Dublin Lying-in Hospital, dur- ing his Mastership. {System cf Midwifery ., p. 509.) Dr. Lohrer of Vienna says that he met w^itli it only twice out of 50,000 new-born children. {Constatfs Jaliresber fur 1842. Band I. S. 456.) Notwithstanding these statements, I am of the opinion that these malformations in some form or other are of much more frequent occurrence than is generally conceded, and that ma- ny children born with some one or other of them, are sufiiered to perish for want of proper and timely surgical assistance through either the ignorance, the neglect, or the mismanage inent of midwives and monthly nurses, l^one doubtless but the most desperate and the most remarkable cases are evei reported, the rest being either entirely overlooked, or passed by unrecorded. But few cases appear to have occurred to the older surgeons, in consequence no doubt of the general employment of ignorant midwives, who, even if they discov- ered them, never revealed nor recorded them. These several circumstances may account for the paucity of information up- INTRODUCTION. 41 on tliis subject among the old, and to some extent also among the modern surgeons. It is therefore impossihlc IVom the data before me to draw any satisfactory conclusions on the subject. SECTION III. ETIOLOGY. "With regard to the primary cause which determines these or other congenital vices of conformation, nothing of a defi- nite, or of a satisfactory character has yet been ascertained. The science of embryology which is now being so successfully cultivated, teaches that at any period during the evolution of the embryo or the foetus, the action of the formative energies in any part of the organization, may be so aifected, or so influ- enced, as to become either partially or wholly suspended, or augmented, and result in the production of imperfect or anom- alous organs, or in an entire want, or non-production of them. This is doubtless the source of many of the congenital mal- formations observed in the anus and the rectum ; but as the first or primary cause of this disturbance, or of this interrup- tion of the plastic forces, is yet beyond our knowledge, and merely conjectural, all in relation to it therefore, is hypoth- esis. Might not the result of power acting upon the foetus in utero through the imagination, or the feelings of the mother, be the cause of malformations ? Is it at all possible for the 'maternal imaginatio7i to be so wrought upon as to cause a partial or a total arrest of development, or an excess of devel- opment in any portion of the foetus ? Will any one deny that a sudden fright of the mother might not be sufficient to destroy the life of the foetus? or refuse to admit that vivid and prolonged impressions of the mother, of whatever cliarac- 42 INTRODUCTION. ter, miglit not give rise to disease in the foetus, and such disease ultimate in tlie malformation of some organ ? Might not some of these malformations occur associated with certain congenital and hereditary diseases, in the relation of cause and effect ? MM. Serres, Geoffroy Saint-IIilaire and Eoux de Brig- noles, concur in opinion that the congenital malformations of the anus and the rectum depend upon the deviation, the imperfection, or the absence of the hfemorrhoidal arteries. Indieed their opinion is that the evolution of the organs in the foetal state proceeds in a strict ratio with their supply of blood ; consequently that the imperfection, atrophy, or absence of the organs generally, is attributable to the imperfection, or the absence of their nutrient arteries. According to M. Serres, the incomplete development, or absence of a part depends upon deficient development of the artery which should convey to it the materials for its nutri- tion. If the artery is only partially developed, the part to which it is distributed remains in a state of atrophy ; if it is totally wanting, the organ does not exist. M. Beclard in com- menting upon this last assertion of M. Serres, says that it seems natural enough that the artery of a part should be want- ing, when the part itself did not exist, and that it seemed impossible for him to decide which of these two facts, the absence of the organ, or the absence of the artery, was the cause or the effect ! Tiedemann, on the contrary, believing that the nervous sys- tem was developed before any of the other parts of the body, was of opinion that congenital malformations or anomalies depend upon the imperfection, or the want of certain portions of the nervous system. He found that whenever certain por- tions of the nervous system were defective or missing, the part to which such nerves were, or would have been distrib- uted in the normal state, was also correspondingly defective INTRODUCTION. 43 or wanting-. lie is of opinion that tlio nervous system con- trols the Ibrnuition and development ol" the; embryo, and determines the particular form and disposition of the organs — hence he concludes that most deformities have their fii-st cause in the irregular development of this system. (London Medical and Physical Journal^ July, 1820. Also Edinburgh Medical and Surgical Journal, January, 1829.) Tiedemann, in my opinion, has by no means proved clearly, as he pretends to have done, that the nervous system is devel- oped before the sanguineous, that it determines the particular form and disposition of the oi'gans, and that its imperfection is a first cause in the production of deformities, &c. The evi- dences, on the contrary, are decidedly in favor of the view taken by M. Serres, namely, that it is the imperfection of the arterial system, -svliich, in fact, exerts such powerful influence in the production of malformations. M. Andral sets forth the principle that whenever a part of an organ is imperfectly formed, or found to be partially or wholly wanting, those parts that precede it in the normal state have themselves undergone an arrest of development, to a greater or less extent. {Precis d'' Anatomic Pathologique, tome 1. p. 109. Paris : 1829.) But these highly distinguished authors entirely fail to give the primary cause of these malformations. The question still remains unanswered ; and it might still be asked them too, with propriety — what is the cause of the deviation, the imper- fection, or the absence of these arteries, or of these nerves ? A logical mind can hardly be satisfied with the explanations they have given. The truth is, that all we hnoio with cer- tainty is, that we hnow nothing certain on the subject ; and it yet remains a problem for future organologists to solve. Some of the organologists endeavor to prove that all con- genital malformations or anomalies have their origin in " arrested development,^'' which theory is now erected into a 44 INTRODUCTION. law by Meckel and Geoffroy Saint-Hilaire, and most ingen- iously illustrated by Serres in his various wori^s on transcen- dental anatomy, and by Isodore Geoffroy Saint-Hilaire {tlie son) in his work on Teratology. Tliis theory has been carried BO far that some of its enthusiastic advocates even contend that " a woTYian is only an imperfect or incomplete man / a man arrested in his develop') nent.^^ This law, however, fails to apply to a number of the congenital irregularities of struc- ture, of not unfrequent occurrence, so that M. Isodore Saint- Hilaire has been compelled to add another law — that of " execs de developpement^^ in order to account for some of these anomalies ; his father Geoffroy Saint-Hilaire, however, attrib- utes all such to certain accidents during foetal life ; whilst Meckel reo-ards them as the results of disease in the ovum. But it was not my intention, neither does it fall within the scope of this work, to enter minutely into the subject of the cause of these congenital imperfections; and as I have 'per- haps already devoted too much time to it, I must not any longer detain the reader by instituting any further examin- ation into the theories of these authors ; nor into that which attributes all the congenital defects to the principle " of the original germ heing imperfect / or of its becoming so after impregnation^ Those readers who wish to know more on this most important and curious subject, and to trace the her- culean labors of the distinguished organologists, the immortal Geoffroy Saint-Hilaire, who was one of the most profound and indefatigable men of France in his day : the celebrated Prof J. F. Meckel of Halle in Germany, whose reputation as an anatomist and as a man of profound science is unequaled, and M. Serres one of the most accomplished and distinguished anatomists of France, will find it of infinite advantage to con- sult their writings. There are some of the congenital malformations of the anus and rectum which do not depend upon either an arrest of, nor on an excess of development, but are the result of disease in INTUODUCTION. 45 iiitra-utcriiie life. A few such cases have coiue under my own observatit>u. For instance the anornuil narrowing or contraction of the anus, which is sometimes observed in new- born children, and which, when attended with more or less thickening and induration of the integument, is the result of inflamuuition of the anus during foetal life. At other times this congenite contraction is caused by a preternatural activity of the sphinctores ani muscles. In such a case the coarctation from being at first purely spasmodic, may gradually become organic and permanent. Obliteration of the anal aperture, or of the rectum for a greater or less distance above the anus, may be caused by rectitis during foetal life. In such a case the inflammation within the rectum causes, in process of time, a coalescence of its parietes, and thus produces the malformation in question. The same may ultimately result froin permanent contractions of the anus and the rectum. Peritonitis may occur during intra-uterine life, giving rise to adhesions between the intestines, aud to effusion of lymph and serum into the abdominal cavity, and thus occasion mal- formations, if not the death of the foetus. M. Desormeaux records the case of a child whom at birth displayed all the evidences of violent enteritis, but afterwards recovered. He is of opinion that the congenital contractions and obliterations of hollow canals — such as the oesophagus, intestinal canal, anus and urethra, &c. ought to be referred to the influence of previous inflammation. {Dlctionnaire de Medicine de Paris, tome XY. j). 403.) Dnges relates the case of a new^-born child, in whom the abdominal viscera were found agglutinated by a yellow col- ored and firm lymph. There were false membranes on the liver, the spleen, the bladder, &c. The epiploon was adher- ent to the intestines, which were agglutinated into a lump, were yellow, hard and thick. {ReoherGhes sur les Maladies 46 iNTRODUCriOKi les plus importantes et les moins connites des enfans noit- veaux — lies. Paris. 1821.) Otlier instances, of the eflfects of former inflcanimation in the intestines of new born children, are related by the following au- thors — M. Billard. {Traite des Maladies des Enfans nmtveaux — iicset d la Mamelle, p. 441. Paris. 1828.) Cams. {Lehrhuch der Gynah>lag.i^. Band. 11. S. 251. Leipzig. 1820.) M. Cruveil- hier. {Anatomie PatJiologiqae dii Carps Ilamain. Livraison. XV. PI. XI. p>. 2. ols. 2. Bruxelles : 1833.) It is not easy to determine to what cause these diseases of intra-uterine life should be attributed, at a time when the foetus in utero is so completely protected from all those influ- ences from without which may induce inflammation after birth. Sex has been supposed by some to exercise great influence in the production of defective congenital develojjments. It is most certainly true that malformations are most common among males ; but why it should be so seems to me not easy of explanation. SECTION lY. ANATOMICAL AND PATHOLOGICAL CHARACTERS. The congenital malformations of the anus and the rectum present a great variety of forms, from the most simple to the most complicated, so that it is by no means an easy task to enumerate and to describe them, M. Guersant says that he has ■ operated on more than thirty cases, and that each and every case was dissimilar. {Gazette des Ilopltaux. No. LXX. p. 280. Paris : 1857.) I will now consider the anatomical and the pathological conditions which constitute the most common of these vices of structure. INTRODUurloN. 47 1. The anus may be more or less prctcmaturally naiTowed at its margin and sometimes for a short distance above. This congcnite coarctation, in such cases, is most always organic or structural, yet sometimes, though not often, it is purely spas- modic. 2. The marginal integuments of the anus may sometimes extend over the border of the sphincter ani, thereby inducing both deformity and contraction. 3. The anus and the rectum may be normal, but the simple thin and delicate membranous septum of foetal life may still exist, and thus produce a complete occlusion of the anal ori- fice. The anal aperture too, is sometimes completely closed by a very thick and hard membrane, or a substance analagous to it. 4. The anus may be entirely absent, no sign whatever indi- cating where it should be ; the scrotal raphe being continued without interruption back to the coccyx. In such a case the rectum may also be partially or entirely absent, and the sphinctores ani, may or may not be present. 5. In the absence of the natural anus there may be a pre- ternatural one, performing the functions of an anus, and occupying some extraordinary situation. In these instances the rectum may be partially or totally absent, and the colon also may be wanting. 6. The rectum at some point in the pelvis more or less distant above its natural outlet, may terminate in a cul-de-sac, and either hang loosely or be attached to some of the sur- rounding parts, there being no indication wdiatever of an anus. 7. Tlie rectum may be interrupted at a variable distance above a naturally formed anus, by a thin or thick annular membranous septum like a diaphragm. Sometimes it is com- pletely closed at several points by such membranous septa, its diameter, however, at those points remaining undiminished, 48 INTRODUCTIO?r. and the canal, with the exception of these j)artitions being entirely natural. 8. The anus being normal, the rectum for a greater or less distance above it, may degenerate into a solid mass resem- bling a cord, or be entirely wanting ; or this degeneration may be confined only to its superior portion, and reassume its cylindi'ical shape again as it approaches the anus, forming, as it were a pouch at its inferior extremity. 9. The rectum may be completely obliterated throughout its whole extent, by a thickening of its coats, its walls approx- imating and firmly adhering as though glued together; or this obliteration may take place at one or two points only in the course of the rectum, the canal at these places appearing as if tied with a tape ; the anus and intervening spaces being natural. 10. The rectum may be present and present its cylindrical form, whilst its cavity may be completely blocked up with a substance of a cellulo-fibrous character; no anus being present. 11. Tlie rectum may terminate in the bladder or the ure- thra ; or in the vagina, or the uterus ; or in a cloaca in the perinsEum, with the urethra and the vagina. In these in- stances there is generally no sign of a normal anus ; yet some- times, though rarely, it does exist, and permits the introduc- tion of the end of the probe for a few lines. 12. Tlie rectum may terminate in the sacral region by an abnormal anus ; it may be prolonged in the form of a fistulous sinus, and terminate by an abnormal opening at difterent points in the perinaeum ; at the glans penis, labia pudendi, &c. In these cases the normal anus is generally absent. 13. The rectum may be entirely wanting and its place sup- plied by a fatty cellular tissue. In these instances the colon ends in a cul-de-sac, with or without a ligamentous appendage in continuation, and is either ^dherent,or floats loosely in the INTKODUCTION. 49 pelvic, or abdoniiiuiml cavity. No iionnul {iims exists, but sometimes an abnormal one does. 14. The rectmn and the colon may botli ])o absent. In these instances there is no natural anus, but often a preterna- tural one situated in some unusual or extraordinary region of the body, communicating either with the cajcuni or some portion of the small intestines. 15. With any of these malformations there may coexist iu the same patient a further deformity of some of the neighbor- ing sexual organs in a greater or less degree ; or of some arrest of development — as fissure of the scrotum, witli the glans penis and the meatus in the perinaeum, spina bifida, the absence of a portion of an extremity, &c., &c. I here consider it important, for the better understanding of the subject, to give a short retrospective view of the history of the development of the rectum and the anus. These two organs, the rectum and the anus, in their evolu- tion, like other portions of the organization, pass through several types and degrees of development before they attain that perfect form and arrxingement destined to represent their permanent condition. The formative process may be impeded at any one of these stages of development, and cause such derangement of their evolution, as would more or less interfere with their normal growth, and exhibit at birth the precise character which was impressed upon them when the liinderance first occurred. In the early period of fcetal life the rectum and the amis are isolated, the former is lodged in the abdominal cavity, but it gradually descends into the pelvis to meet the latter ; tliey both continue to progress, and to approach each other, attain- ing their proper dimensions by successive accretions, the first from the mucous and the second from the serous layer, and in due time their extremities meet and coalesce, and the common conduit is thus formed. Should arrest of development occur at any period during this natural process, in one or the other of 50 IXTKODUCTION. these organs, or in both of them at the same time, various malformations peculiar to each might be produced. The rectum during embryonic life is confounded with the bladder, the urinary and genital canals terminating in one common cloaca — Whence a derangement of the formative pro- cess, at this period, in either the rectum, or in any one of the genito-urinary organs, might cause one or all of them to be more or less defective — resulting in either a limited or an ex- tensive imperforation of the rectum, or in some anormal com- munication between it and the bladder, the urethra or the '? vagina. At an early period of foetal life the anus, together with the other external openings of the body, is covered with a peculiar skin, somewhat analogous to that which covers the surface of the body. Tliis skin, should the evolution of the fostus go on naturally, becomes gradually thinner, appearing ultimately as a peculiar secreting membrane, and is finally removed from its situation over the anal orifice by absorption. Should this normal process of absorption be arrested, or cease to go on, however, this skin or membrane would remain stationary over the anal aperture and consequently form an atresia ani. It will thus be seen that in such instances of imperforation of the anus, that the occluding skin or membrane was, in the early stage of foetal existence, a normal formation. rSTUODUCTION. 51 SYNOPSIS. The Congenital Malformations ^ of the Anus. 1. Preternatural narrowing. 2. Occlusion by a tliin int'inl)rane. 3. Occliision by a thick hard nicmbraiic. 4. Partial or complete absence. 5. Abnormal. Occlusioyi of the Meet am. Obliteration of the Mectuniu The Congenital Malformations \ of the, Rectum. Preternatwral termination of the Rectum. Pretematiival termination of other organs %n the Rectum, "1. By one membranous septum. 2. By two or more mem- branous septa. '1. By the agglutination of its parietes, 2. By the j)uekering of its parietes. 3. By the thickening and the induration of its parietes. 1. In a cul-de-sac. 2. In the bladder. 3. In the urethra. 4. In the vagina. 5* In a cloaca in the peri- naeum with the vasri- na and urethra. 6. In the ano-perinteal region, at difierent points. 7. In the sacral region. 1. Of the ureters. 2. Of the vagina. 3. Of the uterus. Absence of the ( 1. Partial. Rectum, {I: Complete. 52 INTRODUCTION. SECTION V. CLASSIFICATION. Taxing as a basis of classification, the anatomical and tlie pathological condition of the various congenital malforma- tions and imperfections of the anus and the rectum, I will dis- tinguish them all into nine species, each one of which may comprise a greater or a less number of varieties. In this ar- rangement I have considered convenience and usefulness ra- ther than an appearance of scientific precision, I am well aware that it is not perfect, but I trust it will be found sufii- ciently plain, comprehensive and correct for all practical jjur- poses. Tliis division corresponds somewhat to that suggested by Papendorf many years ago, whose divisions and definitions of the congenital malformations of the anus and the rectimi^, although quite imperfect, yet, are, for the purposes designed, as good as any I have observed of a later date. {Dissertatio sistens observationes \de ano infantum imperforato. Lugd, Batav. 1781. Uo.) FIEST SPECIES. This species consists of a preternatural narrowing of the anus at its margin, and occasionally extending a short distance above this point. SECOND SPECIES. In this species there is a complete occlusion of the anal aperture by a simple membrane ; or by the common integu- ment, or a substance analogous to it, more or less thick and hard. TIIIKD SPECIES. In this species there is no anus whatever, the rectum being partially deficient and terminating in a cul-de-sac at a greater or less distance above its natural outlet, without any commu- nication whatever, either externally or internally. TNTRODUCTIOJr. 53 FOURTH SPECIES. The anus in tliis species is normal, but the rectum at vari- able distances above it, is either deficient, obliterated, or com- pletely obstructed by a membranous septum. FIFTH SFECIES. In this species the rectum terminates externally by an ab- normal anus, located in some unnatural situation, as at some point in the sacral region ; or the rectum is prolonged in the form of a fistulous sinus and terminates by an abnormal anus, at the glans penis, the labia pudendi, or at different points in the perinagum. The natural anus being generally absent, its functions are performed by the abnormal one. SIXTH SPECIES. Tlie rectum in this species opens preternaturally into the bladder, the urethra, or the vagina ; or into a cloaca in the perinseum with the urethra and the vagina. In these instances the normal anus does not generally exist. SEVENTH SPECIES. In this species the rectum is normal, with the exception that either the ureters, the vagina or the uterus, open preter- iiiiturally into it EIGHTH SPECIES. In this species the rectum is entirely wanting. NINTH SPECIES. In tbis species the rectum and the colon are both absent, ,and there is usually an abnormal anus situated in some extra .ordinary part of the body. '.54: INTKODUCTION. SECTION VI, GENERAL SYMPTOMS. Should any of these congenital vices of structure have jm- fortunately escaped the observation of the accoucheur or the nurse at the time of the hirth of the child, its existence in the majority of instances would sooner or later manifest itself by a train of morbid phenomena simulating, strangulated hernia,, the result of the retention of the meconium and other matter. K no alvine dejections take place within twelve or twenty- four hours after birth, the child gradually becomes restless,, and by its peculiar plaintive cries manifests the suifering it now begins to endure. These cries are generally attributed by the nurse, to colic, and the little suiferer is treated accord- ingly with all kinds of medicines, but generally to none but the worst of purpose. The abdomen, especially in the hypo- gastric region, now becomes enlarged, tense, hot, shining, and painful upon pressure, the respiration becomes difficult and irregular, and the pulse frequent, small and contracted. To these symptoms, if no amendment soon takes place, vomiting will be added, first, of all the milk and other fluids swallowed, then of the mucous and biliary secretions, and finally, of the meconium, or a dark brownish matter analogous to it» Should no relief still be afforded the little sufferer, these symptoms will become augmsented in violence ; the diaphragm and other abdominal muscles will become excited to violent expulsive efforts, during which respiration will sometimes become suspended, the face will become swelled, discolored and covered with perspiration ; the voice sooner or later will become almost extinct ; there will be hiccup, with coldness- and flexure of the extremities and convulsions. In the male,, inflation of the scrotum and penis sooner or later takes place. Should matters thus continue, death is inevitable and is soon ushered in ; and it usually takes place between the third and the eighth day, according, to the vigor of tlie little patient. INTliODUCTION. 55 Before death occurs there is often a ^^encral yellowness oi' tlie skin. When the case is protracted for a number of days the emaciation becomes extreme, and the patient dies from the etfects of inanition. Strange to say, that cases of complete occlusion of the rec- tum have occurred, in which life had been prolonged for a number of days, and even for months witliout any evacuation from the bowels, and before any violent symptoms had taken place. Wolf mentions a case of imperforation of the anus and rec- tum in which, strange to say, the deformity was not discover- ed and no unfavorable symptoms manifested themselves until the evening of the twelfth day, the child during this time not having had any motion from its bowels, when it was attacked with vomiting, hiccup and convulsions, attended with disten- tion and hardness of the abdomen and great prostration. [Yide Case LIX.] A still more remarkable case of imperforate rectum is re- ported by Dr. A. B. Shipman of Courtlandville, in the State of New- York. In this instance the child lived three months without passing anything from its bowels. He says the child was nearly as large as ordinary children of that age, and was not afflicted with vomiting or crjang more than many are, who are considered healthy. [Yide Case XXIX.] Mr. West says that Mr. Arnott communicated to him a case in which the child lived seven weeks and three days, the rec- tum being entirely absent, and the colon terminating in a blind sac, and floating loosely in the abdominal cavity. {Ojj. cit.p. 376.) De La Marre mentions an instance of a child having an anal imperforation, which lived six months without ever having had any evacuation from its bowels. In this case the milk and everything else taken into the stomach were constantly ejected by vomiting. {.Journal de Medlcme de Paris, annee. 1770. tome XXXIIL ^. 510.) 56 INTBODirCTION. A case is reported iii tlie " Provincial Medieal and Surgi- cal Journal " for March, 1851, in which a child having an im- perforate anns lived one hundred and two days without hav- ing any evacuation from its bowels, and dm-ing this time never vomited. Death in instances of imperforation of the anus or the rec- tum, is usually the result of enteritis, peritonitis and intestinal paralysis. Sometimes previous to death in consequence of the violent expulsive efforts to overcome the obstruction, the colon, or some other portion of the intestinal canal bursts, and its con- tents are poured into the peritonseal cavity, death being ushered in by the sudden supervention of a state of collapse. A. case of this kind is related by M. Fourcade. {RevueMedi- cale de Paris, annee. 1830. tome VI. y. 52.) On dissection, the intestines will be found enormously dis- tended with gas, meconium and other matters, and highly inilamed. The distention or tympinitic state of the abdomen in these cases is caused, in part, by the disorganization which, at an early period takes place in the contents of the intestines, by which great quantities of gas are disengaged. The intestinal nerves become affected, hence the spasms. The blood vessels of the lower extremities too, become compressed, and this comj^ression induces congestion of the heart, lungs, and brain. This phenomenon is very evident when the distended cavity of the abdomen presses upon the thoracic viscera. The com- pressed lungs no longer admit full respiration ; the vital transformations of the blood are inadequately made, and at the same time, as the excrementitious matters of the body cannot be carried off by defecation, the composition of the blood becomes such as no longer to afford any nourishment to the vital organs. Conjointly with the general signs of intestinal obstruction, there are in each case some special indications of the peculiar INTRODDCrriON. 57 form of niixlforination to which the obstruction is due. These special symptoms will be fully given in the following clia})ters, on the different species of malformation. The pathognomonic sign is obtained by the direct inspection of the anus and the rectum. SECTIOi^" VII. PROGNOSIS. Anciently the malformations of the anus and the rectum, together with those of the genito-urinary organs, were looked upon as necessarily fatal, and the unfortunate victims of them were regarded in the light of monsters, and left to perish. Even at tlie present day this sentiment prevails to a certain extent, and the subject is still surrounded by no inconsider- able degree of mystery, the most insignificant deviations from the natural standard being apt to be exaggerated and invested with an importance which by no means legitimately belongs to them. When we take into consideration the fragility of the sub- jects, the deplorable nature of some of the species of these malformations, and the formidable character of some of the operations 'necessary for their relief, the hope of ultimate suc- cess does indeed appear but slight ; yet such are the great improvements that have been, and are being made in modern surgery, that the evil is by no means deplorable, even in some of the w^orst cases, as will be shown hereafter. 'No case should be abandoned in despair, although surrounded by the most discouraging circumstances. Many of the cases may be relieved immediately by simple and appropriate trea-tment, and others admit of certain relief, by prompt surgical meas- ures, which not only save, but prolong life, Tlie surgeon 58 INTRODUCTION. must be very careful, however, not to promise the parents or the friends of the child too much even in the most simple case, recollecting how natural it is for them to imagine that if the operation succeeds, all will be well, and that the child will be left in every respect perfect. This would be a great mistake, as every surgeon knows who has had any experience in endeavoring to remedy defective formations. Therefore, to prevent misconception on this point, and the evil conse- quences of it, the surgeon must previously explain to them that the operaition may indeed afford an outlet and immediate relief ; but that such an artificial opening or anus, not being formed by nature for the specific purpose, cannot be expected to possess all the powers or to perform all the functions of which the natural anus would have been capable. The most favorable cases of course are those which require the least surgical assistance — such in which there is a con- traction of the anal orifice, and requires but simple dilatation, or such in which the anal orifice is obstructed by a membrane which only requires to be divided. Tlie most formidable cases are those in which there is a considerable deficiency, or an entire absence of the rectum, and in which there exists no outlet whatever. In all such cases, without an operation, death soon takes place from necessity. Some surgeons, however, consider all such cases necessarily fatal, and beyond the power of art to remedy : yet, as I will hereafter show, even a number of such cases have been relieved, by either the operation of proctoplasty or colot- omy. In such a case even a doubtful remedy should be 2)referred and attempted in preference to the certain death of the infant, Tliose cases in which the rectum opens into the bladder by an abnormal anus, or into the urethra, or the vagina ; or in which there exists a preternatural anus on some part of the body, are not so formidable and do not terminate in death so quickly. Some of them may be entirely relieved, others INTRODUCTION. 39 greatly benefitted, whilst otliera again admit of palliative treatment only. Some very remarkable cases are recorded of life having been sustained and prolonged for days, months, and even vears, in which no anus whatever existed, nor in which had any operation been performed. In these instances there was consid(^-able deformity too of the genito-urinary organs, A man forty years of age was seen by Bartholin, in whom no anus existed, but who discharged his fseces from his mouth by means of a horn, made for the purpose, and who voided his urine from the umbilicus. {Historia Anatomicce, cent. I. ohserv. LXV. f, 113.) Baux saw a girl fourteen years old who had neither an anal, a genital, nor a urinary opening. There was not the least appearance of these apertures, the skin being smoothly contin- ned over the situation naturally occupied by them, as on other parts of the body. At the end of every third day she experi- enced considerable pain around the umbilicus, and immediately after would eject faecal matter by vomiting. Her urine was entirely voided by the nipples every three or four hours. This girl was well formed in other respects, and of a veiy agreeable person. She had a good appetite, slept well, and had general good health. {Journal de Medicine de Paris tome YIII. J). 59.) These, however, are extraordinary cases, they form the exception to the rule, and they must not lead the practitioner to the conclusion that in cases similar no operation for their relief should be undertaken. !No one will dispute the neces- sity of an operation in a case of atresia ani, because single cases have been known to exist in which children have lived for days, months, and even years without such surgical inter- ference. Tlie observation made by the celebrated Callisen many years ago, still stands firm, and must not be forgotten. " The. atresia ani," says he, " will certainly be followed by death, unless a passage is formed and maintained." (Sy sterna Chii'urgie^ Hod. tome II. p. 840. Hqfnice. 1800.) 60 mTRODUCTION. The operation for the establishment of an artificial anus, either in the perinaeum, or in the abdomen, seems so grave a one for a child at so tender an age, that many surgeons decline it altogether. This consideration alone, however, should by no means deter the surgeon from operating, for it is an established fact, and the knowledge of it should be more universally known — that children sustain an operation much better soon after birth, than at a later period. This is doubt- less in consequence of the small vital development of new- bom children, who, in this respect, are similar to the inferior animals. This analogy rests upon the recuperative power common to them both, by virtue of which wounds in both are followed by very slight inflammation, or even none at all, and show a direct tendency to heal by the first intention. CH^I^TER II. THE FIRST SPECIES OF MALFOEMATION. SECTION I. DESOKIPTION. 1. This specieis of congenital malformation is characterized, as has been already observed, by an abnormal narrowing of the anal orifice, which contraction, however, is by no means always confined to the verge of the anus, but is occasionally found extending up into the canal itself, and consisting some- times of numerous folds projecting into the cavity of the rectum, and which, according to their degree of development, more or less obstruct the physiological functions of it. Some- times the marginal integument of the anus extends over the border of the sphincter muscle and thus produces both con- traction and deformity. 2. This congenital narrowing is usually organic, being attended with more or less thickening and induration of the integument about the anus, the result doubtless of previous inflammation; at other times however, the contraction is purely spasmodic, depending upon a peculiar condition of the sphinctores ani muscles which are found to be preternatu- rally active. 3. The anal opening and the cavity of the rectum, in these instances of congenital contraction, may present all the diflerent deo-rees of stricture, from that into which the point of the smallest probe cannot be introduced, and impossible for the meconium to pass, to that which opposes no obstruction w^hat- 62 THE FIRST SPECIES OF MALFOEMATION. ever to the common sized probe, and but little to the passage of the meconium or the excrementitious matters. 4. Tlie situation and the form of the anus in this species of malformation are generally normal, but the preternaturally contracted or puckered-up orifice, always presents the pli- cated appearance of the mouth of a purse tightly drawn. 5. The signs of the congenital coarctation of the anus, or the rectum, are the absence or the deficiency of the meco- nium in the napkin which the child wears, the progressive and painful tension of the abdomen, and vomiting. The pathognomonic sign is furnished by the direct inspection of the anus. 6. There is one variety as it may be termed, of this species of malformation which must not be omitted here ; it is the anal contraction sometimes observed in new-born children who have a syphilitic taint which is the cause of it. It is of the utmost importance that the surgeon or the practitioner of midwifery should make the distinction between it and the other varieties, as it requires an entirely difi'erent treatment. His attention will be first called to it by some of the same signs which characterize the other varieties of this species — such as pain, severe straining efforts and difficulty, at each evacuation, and a peculiarly small aperture. On a proper examination, however, there will be discovered other signs or appearances which will explain the true nature of the case — such as discolorations of the surrounding integument ; excoriations, and even superficial ulceration in the adjacent structures, with a considerable exudation ; small fissures of the anus, as well as about the commissures of the lips ; soft granulations, or condylomata are also sometimes present at the verge of the anus, discharging a tenacious matter. Other constitutional symptoms are also usually present — such as copper-colored blotches on the skin ; a tendency to crack- ing and excoriation of the skin about the hands, feet and TlIK FIRST SPECIES OF MALFORMATION. G3 nates ; an imperfect development of, or a tendency to a sep- eration of tlie nails ; general emaciation ; suspicious appear- ances about the mouth and tongue, and a very remarkable and peculiar hoarseness in crying. Many, if not most of these symptoms, aided by the history of the parents will lead the surgeon to distinguish this peculiar congenital contrac- tion of the anus, and enable him to make his diagnosis accordingly. 7. There are but few cases of this species of malformation on record — hence many imagine that it is quite rare. I am, however, of opinion that it is much more common than is generally supposed, and the reason that so few cases are reported, is that they are usually so simple in their nature and so easily remedied that no further notice is taken of them by the surgeon. The slight ones too, are doubtless often entirely overlooked. Two cases only of this species have come under my own observation. 8. Immediate attention should be given to children who have a congenital stricture of the anus or the rectum. SECTION II. TREATMENT. 1. The treatment of this species is generally simple, easy of accomplishment and most always attended with success. It is either by dilatation alone, or by incision and dilatation combined, according to the nature and straitness of the con- traction. In all cases in which the common probe can be passed, simple dilatation, if persevered in for a short time, scarcely ever fails to effect a cure, especially if commenced in time. It is not only applicable to the organic contraction, 64 THE FIRST SPECIES OF MALFOKMATION. but equally so to that caused by a preternatural activity of the sphinctores ani muscles. 2. The dilatation should be effected by means of wa'x, gum-elastic or metallic bougies, similar in construction to those used for the urethra, but about two-thirds shorter. I prefer the wax bougie for this purpose, to all other kinds. The bougies should consist of a regular series of gradually increased sizes. The first one should be of such a size as to pass the constriction easily, care being taken not to make too rapid or too great distension, but to use the same instrument for a day or two in succession before exchanging it for a larger one. The bougie should be used once at least in twenty-four hours, by simply passing it through the contraction, and then immediately withdrawing it. Prolonged dilatation — that is, the retention of the bougie for a length of time, I repudiate in such cases. An enema of warm flax-seed tea with a little pure olive oil in it, should be administered about an hour pre- vious to using the bougie, in order to empty the rectum, and prevent the dangerous accumulations which are liable to take place, as well as to facilitate the introduction of the instru ment. The bougie should always be warmed and well lubricated with simple cerate previous to its insertion. 3. This course should be persevered in until the orifice has acquired it normal size, or until the full amplitude of the canal is restored. It is important, however, even after the dilatation has been carried to the full extent, to use the bougie occasionally in consequence of the disposition of the orifice sometimes to contract again. It should therefore be closely watched for some time afterwards. 4. Should any undue irritation or inflammation be excited in the parts during the process of dilatation some soothing means should be used to allay it — such as warm mucilaginous and opiate enemata, frequently repeated, or the repeated employment of the warm hip bath which is one of the very best means for this purpose ; indeed the frequent employ- THE FIllST SPECIES OF MALFOKMATION. 65 meiit, during the use of the bougie, of warm injections of the decoctions oi althea or Jlax-seed^ conjoined with the warm hip- bath, would greatly tend to, if not entirely, prevent irritation or inflammation. 5. In the treatment of some of these cases, the little linger of the child's mother or nurse if eitlier of them is intelligent, might be substituted for the bougie, after the orifice has been sufficiently dilated by that instrument to admit the finger. The finger would greatly aid the bougie in over- coming the stricture and preventing its return, being one of the best instruments for that purpose, as it can be so easily insinuated into the orifice, and in such a manner too, as to cause but little, if any pain, and no injury. 6. The congenite contraction in some instances is so slight that it is apt to be overlooked or neglected during the whole period of infancy, and in other instances the treatment is abandoned too soon, or before the dilatation has been carried far enough ; all owing doubtless to the fact that in infancy the faeces *are quite thin or soft, and small in quantity, and expelled with comparative ease, and with but little pain even through a small orifice. This immunity from imme- diate difficulty and danger will not always exist, however ; for as the child advances in years, the f;»ces becon:ie more abundant, more consistent or solid, and consequently more difficult to expel through a small aperture — hence it is highly important to treat those cases, at an early period, even if there should exist but slight obstruction to defecation, for the evil consequences resulting from such neglect, in the after life of the little patient, should never be lost sight of. M. Boyer relates two very interresting cases of this character, in wliicli the congenital narrowing had been either overlooked or neglected in infancy. One was a male eighteen years of age, the other was a female thirty-four years old. Both were cured by incision and dilatation, and both sufi'ered severely every day of their lives previously. {Traite des G6 TilK FIRST SPECriOS OF M \LFOKMATION. Maladies Chirurgicales. tome. F/.j^. 406. P«m, 1S49. Cin- quicme Ed.) 7. In extreme congenital narrowing of the anal orifice, in which the contraction is so small, rigid and unyielding, that it would be most difiicult if not absolutely impossible to insinuate even a small probe, incision is essential to success, especially if considerable time has been suffered to elapse, and the symptoms have become urgent. Here the process by dilatation alone, is too slow, as the child is in imminent danger of perishing from the effects of the accumulation and the retention of the meconium and other matters, and requires immediate relief. The indication in such a case is to make one or two lateral incisions of just sufficient extent to afford complete exit to the contents of the intestines ; to keep the orifice and canal pervious by the use of soft tents and subsequently, if necessary, to complete the cure by dilatation. A slight incision on each side should first be made with the sharp-pointed bistoury to allow a passage to the pent up feecal matters ; an enema of warm flax-seed tea should then be administered so as to unload the rectum completely, and afterwards the incisions should be enlarged if necessary, by the probe-pointed bistoury, either with or without the director, according to the extent of the contrac- tion. If the director is used, it should be introduced to the depth of from five to eight lines, with the bistoury carried on its groove, its handle drawn outwards, that the extremity' of its blade may press in the groove of the director ; and then it should be drawn obliquely downwards and outwards toward the ischiatic tuberosity in such a manner that the inferior part of the incision may extend out from two to four lines from the verge of the anus. The opposite side should in like manner be operated on. In making these incisions care should alwavs be taken, not to extend them out too far lest all the muscular fibres of the spliincter be cut across, causing them to retract and pulling the edges of the incision ♦ THE FIKST SPECIES OF MALFORMATION. 67 too far from each other, and thus giving rise to an ever after, or long continued, troublesome, involuntary discharge of fseces. To avoid this great evil, some of the muscular fibres should always be left undivided, and the cure finished by dilatation. In order to prevent the reunion of these divided parts and to keep the orifice and canal pervious, tents made oi patent lint,, well besmeared with simple cerate, or dipped in glycerine should be introduced, kept in situ by the T bandage, and removed frequently and fresh ones inserted. After using the tents for several days, the bougies should be used daily until the orifice and canal are sufficiently dilated, and the cure completed. 8. I wish it distinctly understood that I protest against incision except in exti-emely urgent cases ; for it is an indu- bitable fact that the smallest contraction may sooner or later be overcome by gradual dilatation ; and it is also equally true, that even after incision has been performed, dilatation is absolutely necessary in almost every case to complete the cure. 9. When the anal stricture is the result of a riirid or powerful contraction of the sphinctores ani muscles, and nu time left to practice dilatation on account of the urgency of the symptoms, a division of some of the fibres of those muscles will at once be required : in all the instances, however, in which it exists in a mitigated form dilatation will relieve it, and render the operation of division unneces- sary 10. When the malfonnation consists of an extension of the marginal integument of the anus, this should be nicked in several places, or divided in several places with the probe- pointed bistoury, from within, outwards, and a meche of charpie besmeared with simple cerate introduced, and constantly worn for several days ; then the bougie should be used until the cure is finally accomplished. 11. The syphilitic contraction of the anus will generally 68 Tim FIRST SPECIES OF JIALFOKSrATKMST.. yield to an alterative course of medicine, such as the nature- of the case shall denote to be neeessaiy. The local difficulty disappears as the constitution is restored to health. Soothing emollient applications are the best topical remedies. Should there be any excoriation or ulceration about the part, the surface should be slightly stimulated daily by a solution of the nitrate of silver, or by the ordinary mercurial lotions^ the' black or the yellow wash^ SECTION III. CASES AND REMARKS. Case i. — On the 21st of January^ 1848, 1 was called,, at the request of Mr. W. D. Oreenwood, to see a large and healthy looking male mulatto child, three days old, whose motherj- Sai'ah Fry, was a free woman and resided in an alley between Camp and Magazine streets. New Orleans ; I was told that the child, had taken quite a quantity of molasses and water to purge it ; had not passed more than a tablespoonful of any thing from its bowels since its birth, and that it was con- stantly making fruitless eiforts to do so. Upon examination, I found the situation and the form of the anus to be normal, but its orifice was so contracted that it offered almost the same resistance to the expulsion of the meconium as though it were completely imperforate. The contraction was con- fined solely to tlie verge of the anus. The other organs were all normal. Vomiting had already commenced and there was considerable tumefaction of the hypogastric, as well as of the anal region, the cliild being quite restless and rapidly becoming dangerously ill,, from the retention of the meconium and gas, and the distention of the rectum. I at once deter- mined on the operation, and whilst Mr. Greenwood held the child, properly placed upon his knees, I thrust into the con- tracted anus the straight shaii3-pointed bistoury and made an incision on the right side, of from three to four lines in extent. A large quantity of meconium and gas at once followed the withdrawal of the instrument. The opposite side was tlien incised in the same manner. A warm enema of milk and THK TLRST SPECIES OF MALFORMATION. 69 •Kviiter Avas now thrown up into tlie rectntn, -wliicli wns soon followed by a still I'liilher evacuation ot" nicconiiun and ijas ; after which a tent nia-^'^- Boston: 1856.) Case X. — Dr. Seaverns, of Jamaica Plain, presented to the '■Boston Society for Medical Improvement^ through J. B. Jackson, M. D., September 13th, 1848, a specimen of con- erenital stricture of the anus. The child died at the age of eighteen months, of a dysenteric affection. At birth the open- ing was only large enough to admit a probe. It was gradually enlarged by the aid of bougies. The intestine above the stric- ture was considerably dilated. {Records of the Boston Society for Medical Improvement. Vol. Ill p. 270. Boston: 1859.) Case XI. — M. Devilliers met with a case in his practice, and which he reported to the " Medical Society of Paris,^'' of a child which had both an obliteration of the anus and of the uretln-a. Upon examining the child with care, M. Devilliers found that the malformation arose from ao-gluti nation of the integument at the anus. He cautiously separated the lips of the anus, and the walls of the rectum, for an extent of about six lines with his right index finger, then using a grooved sound, he reached the point where the meconium was, and TIIK FIRST SrECIES OF MALFORMATION. 73 thus conij)let(!ly opened the passai^e. lie attempted in a siniihu- nuumcr to overcome the agghitination of the uretlira, hut failed ; he, however, finally suceeded hy the aid of a small sound. The child died iiftcen days after. No autopsy. {lie- vue Mcdicale de Paris. Mai, 1835.^^. 280). Case XII. — The following case was reported to the " Pen- insular Journal of Medicine and tiie ColUxteral Sciences," by S. L. Andrews, M. D. " In a private letter from my friend, Dr. Baldwin, of Lahaina, Sandwich Islands, I have an in- terestinsj^ account of a case ot congenital contraction of the intestinal canal. As Dr. B. has given me the case more in detail than is needful for your Journal, I have abridged it for your use. The child, a fine-looking, plump female, weighing 8i|- lbs., was born Dec. 5th, 1838. The first indication of any- thing abnormal was the rejection of a little sweetened water given a few hours after birth. On the following morning castor oil was rejected with bilious vomiting. A judicious use of cathartics, including suppository and enemata, the lat- ter sometimes administered through a gum-elastic catheter introduced several inches into the rectum, failed to produce any adequate evacuation of the bowels. Castor oil and other cathartics, and sometimes enemata, only excited vomiting, usually bilious. At length, the contents of the intestines, in a very offensive state, were thrown off by vomiting. All that was passed, per anum, was fragments of hardened meconium, shaped to the intestines, and amounting to several inches in length. The last fragment tapered to a point at its upper ex- tremity. Death on the 13th. '• Diagnosis, contraction of the intestine, which was con- firmed by the autopsy. "The rectum and colon were about half the natural size, or perhaps a little more, except a portion in the middle of the arch, where it was reduced to about half the diameter of that on each side of it. The caecum was natural, but for twelve inches above it the small intestine was small indeed, not larger than the narrowest tape, and the canal too narrow to admit anything solid ; the next six inches, proceeding towards the stomach, was very narrow, but contained a few small pieces of hardened meconium. Eighteen inches above, this was larger, but crowded with viscid meconium. The re- mainder of the intestine to the stomach was twice the natural size. The gall-bladder was large and full. The stomach and upper part of the intestine was filled with a liquid appearing 74 THE FIRST SPECIES OF MALFORMATION. like a mixture of bile and milk. The child had nursed until the last day. "The father of the child, an efficient and devoted missionary under the American Board, has disproportionately short limbs, both upper and lower. He is also afflicted with exostosis. A sister is afflicted in the same manner, and some of the children of both brother and sister have the same morbid state of the bones." — {Peninsular Journal of Medicine and the Col- lateral Sciences. 1839.) CH^I^TER III. THE SECOND SPECIES OF MALFORMATION. SECTION I. DESCRIPTION. 1. This species of malformation, «^ym« orificu arid, is char acterized by the closure of the anal orifice by a thin transpa- rent membrane, somewhat resembling the hymen, through which the meconium may often be seen, yet sufficiently strong to prevent its escape from the rectum. This membrane, or cutano-mucous lamina, however, is sometimes quite thick and hard, and simulating the common integument of the anal region. 2. This vice of conformation is readily indicated by a small soft and fluctuating hemispherical tumor, usually observed several hours after birth, at the natural situation of the anus, caused by the pressure of the accumulated meco- nium and gas against the occluding membrane. It may also be easily distinguished too, by the yielding of the prominence to the pressure of the fingers, and then projecting again when the pressure is removed ; by the tumor becoming larger, firmer and more ap]3arent whenever the child cries* struggles, or makes efltbrts to expel the contents of the bowels ; by a fluctuation more or less evident, as well as a cavity which can be distinctly felt under the occluding membrane ; and lastly by a bluish or livid spot, usually in the centre of the prominence, indicating clearly the position of the anus. Fabricius ab Aquapendente in describing the same deformity says : '• Msi ani locus velliGula abductus est 75 70 THE SECOND SPECIES OF MALFOEMATION. tamen orificii vestigium et taiujentibus persentitur vaeuum intus.''^ {Opera Chirurgica, part 1. Cap. 88. Patav. 1617, I'olia.) 3. This species of malformation is the most simple form of arrested development pertaining to the anus, and it is doubtless the most frequent, yet if the number of cases on record are to be taken as evidence of this fact, it fails entirely to establish it, for there are indeed but few cases reported. SECTIOIT II. TREATMENT. 1. The anus and the rectum, in this species of malformation are most always well formed, including the ^phinctores ani muscles, the only imperfection being the membranous closure of the anal orifice ; consequent!}'- the surgical measures recommended for the relief of this impediment are simple and uniformly successful, if timely adopted. 2. The treatment consists of a puncture and a crucial incision. The straight sharp-pointed bistoury should first be plunged into the most prominent part of the tumor, in the direction of the rectum, through the occluding membrane to the seat of the meconium ; or into the presumed centre of the anus indicated most always hy the livid spot. This puncture will afford an exit to tlie contents of the intestine, and by their evacuation the most urgent symptoms will at once be relieved. The puncture thus made should then be sufficiently enlarged in the antero-posterior and transverse direction with the probe-pointed bistoury, cutting the mem brane from witlun outwards ; and if it be very thick the angles of the flaps formed by the crucial incision should be seized witli the forceps and excised with tlie curved cissors. THE Ki:CO]Sfr> SPECIES OE MALFORM4'riO:Sr. 77 After the complete eviiciuitioii of the distended rectnrn hy warm eiiemata, a tent or meche of lint spread with simjde cerate, or dipped in olive oil should be introduced into the opening and renewed from time to time until complete cicatrization has taken place. It is scarcely ever necessary to use the bougie in these cases, and even the meche of lint may often be dispensed with, after the sixth or seventh day, as there is generally no disposition in the parts to contract too nmch, especially if the membrane has been thin, and the anus well formed as is usually the case. 3. Professor Hays, of Philadelphia, the very able and distinguished editor of the " American Journal of the Medical Sciences," advises the operation to be performed at the moment when the infant makes efforts to expel the contents of the rectum, and the membrane is most tense. He thinks it wholly unnecessary to cut off the angles of the membrane formed by the crucial incision, as they soon retract towards their base and become confounded with the margin of the anus. {Aineriean Cyclo^CBdia of Practical Medicine and Surgery. Vol. II. Article^ Imperforate Anus, p. 151, Phil. : 1841.) 4. Professor Pancoast, of Philadelphia, in his invaluable treatise on " Operative Surgery," says that the employment of bougies, or of catheters, after the operation of opening the anal orihce, for the purpose of keeping open the passage, or enlarging it, is not unattended with dangei", in consequence of the soft and delicate organization of the mucous membrane of the rectum, at this early age — hence he recommends that the newly made opening should be preserved patulous by the daily introduction of the finger previously oiled. {Operative Surgery, p. ^'dQ. Phil.: 1841.) 5. M, Levret recommended, in these cases of anal occlusion, circumscribing the obstructing membrane by a circular inci- sion. This operation, however, is never practised. 78 THE SECOND SPECIES OF MALFORMATION. SECTIONIIL CASES AND REMARKS. Case XIII. — In February, 1840, I was sent for in haste by Mr. H of Bourbon County, Kentucky, at the request of the attending midwife, Mrs. S to see his child, a stout, healthy boy, forty-eight hours old. It appeared that in conse- quence of the feeble condition of Mrs. 11 , who required a great deal of attention, that the child had been neglected, and the discovery had just been made, that it had not passed anything from its bowels since its birth, and that it really had no anal opening. Upon examination I found the anal orifice completely occluded by a tolerably thick brownish mem- brane, surrounded by considerable puckering of the adjacent integument. The obstructing membrane was distended by the meconium and formed a soft projecting tumor as large as a filbert. The child was continually vomiting the milk as fast as taken into the stomach, and its abdomen was slightly swelled and tense. It was perfect in other respects, and urin- ated freely. The cliild was properly placed upon its back on the lap of the midwife who held it firmly with its thighs eleva- ted and nates separated, whilst I plunged a sharp-pointed bis- toury into the centre of the projection, through which opening the contents of the bowels were at once discharged. I then with a probe-pointed bistoury enlarged the opening by incising the membrane from within, outwards and crucially ; the angles of the flaps thus formed were seized with the forceps and ex- cised with a curved scissors. A tent of lint dipped in olive oil was now introduced into the newly made orifice and frequently removed afterwards, and replaced by a new one, until the cure was complete, which took place in less than three weeks. To my surprise, considerable haemorrhage occurred, but not suflicient to cause any bad result. In this case the occluding membrane was of a dark brownish color, quite elastic and about two lines in thickness. I saw this boy in 1854, when he had attained his fourteenth year, and he had as well formed an anus as could be desired. Case XIY.— Gunning S. Bedford, M. D., the able and distinguished Professor of Obstetrics and the Diseases of Women and Children in the Medical Department of the Uni- versity of the City of New York, mentions a case of occlusion of the anal aperture. A male child one week old was brought to the Professor's Gli7iique, ajjparently in great agony, not hav- ing had anything to pass its bowels since its birth, refusing THE SECOND SPECIES OF MALFORMATION. 79 tlie breast and constantly moaning, I prefer presenting a part of this case in the inimitable style of the professor hini- eelf. " That is not your child, madam — is it? No sir ; its mother is too weak to come out. So I should think, my good woman. That little infant is rather young to be brought here. Yes Sir; I know it is, but the poor little dear suffers so much that its mother begged me to let yon see it. Well, madam, we will do what we can for it. Are you certain that it has not had a passage since its birth ? Oh yes Sir — I know it has not. Does it pass its water ? Yes Sir. Have you given it any medicine ? Indeed, Sir, it has taken all sorts of things. What has it taken, madam ? Molasses and water, and castor oil and rhubarb, and — There my good woman, that will do. Why, Sir, I have not told you half. You have told me suf- ficient to satisfy my mind that the poor little infant, young as it is, has passed through a martyrdom ! Does that child vomit ? Oh yes, sir ; for the last four days it could not keep anything on its stomach. Is its little belly large? Oh yes, Sir ; it is very much swelled. Has it been attended by a doctor? Yes, sir ; and he said the child's bowels had the torpids. You mean torpor, do you not, madam ? Well, Sir ; it was something that way. I think we shall discover, my good woman, that the torpor was in the doctor's brain." CFpon examination the professor found a complete occlu- sion of the child's anus, which at once accounted for the uon evacuation of its bowels. " Madam, it is not necessary for me to tell you that this child is in a very dangerous situation. Oh, no Sir ; I see it, poor little dear. There is but one thing, my good woman, that presents the slightest ground of relief, and that is an operation. What, Sir ; to open its stomach? jSTo madam, we do not open stomachs here — and you need have no fear of the operation of which I speak. Shall I do what I think is proper, and which, in fact, is the only thing that can be done? Yes, Sir; I am sure the poor babe's mother will consent to anything. What I propose doing, gentlemen, is to divide by a simple incision, the membrane which you perceive has caused an imperforation of the anus." The child was placed on its back, the thighs elevated by an assistant, and tbe occlusion being well exposed, the Professor with a bistoury, made the incision ; and immediately a large quantity of meconium passed from the bowels ; the tumefac- tion of the abdomen became very much diminished, and the infant's countenance gave evidence of relief. " In order, gentlemen, that the incision I have made may so THE SECOND SPECIES OF MALFOEMATIOX. be kept open, it will be necessary for a day or two to intro- duce into it a small pledget of lint, well smeared with simple cerate ; and it will also be proper to throw up the bowel two wine-glasses of tepid water this evening, with a view of pro- moting a free evacuation," In a subsequent lecture the Professor alludes to the same case again : "You will scarcely recognise, gentlemen, in this infant, the little sufferer brought here some time since apparently in a moribund condition. To be frank with you, 1 am surprised to see it alive. This is the infant, you will remember, with imperforate anus, on which I operated when it was about a week old. At the time when I performed the operation, I very distinctly mentioned that such was the low condition of the infant, I could make no assurance of a successful issue. I am now agreeably disappointed, and this recovery affords another evidence of the extraordinary tenacity of life." {Clinical Lectures ofi Diseases of Woman and Childt'en. Uh Ed. pp. 295, 325. Wew York : 1857.) Case XY. — Mr. Hutchison relates a case of this species : " A male child one day old was brought to the Westminster General Dispensary by the attending midwife ; and as the gut visibly caused a protrusion of the parts, when gentle titillation was made over the situation where the anus sliould have been, which was marked, the point of a lancet was intro- duced about the eighth of an inch or upwards, which entered the gut, and was sufficient to liberate the contained meco- nium. Tills opening was afterwards enlarged with a bistoury; a small piece of lint dipped in oil was now introduced, to pre- vent the sides of the incised wound from again uniting ; and the infant was discharged cured in about three weeks, with a well-formed anus." {Ojj. cit. p. 261.) Case XVI. — ^The following case of simple occlusion of the anal orifice was reported to the " Suffolk District Medical Society of Massachusetts," by E. B. Moore, M.D. " A male child was born on the 22d of jN^ov. 1853. Where the anal opening should have been, there existed a sac projecting three-fourths of an inch from the body of the child. Dr. Moore operated three days after birth with a trocar, and after- wards dilated the opening by bougies, beginning with one the size of a pipe-stem^ and gradually increasing the size until one three-fourths of an inch in diameter could be passed. December 3d, eight days after the operation, the child was dismissed as cured, lie has been generiilly, and is now. THE SECOND SPECIES OF MALFORMATION. 81 (1857) well and hcai-tv." {Boston II edhxil and SurgicalJour- ncd, Vol. L VI L 2>. 510. Boston, 1858.) Case XVII. — M. Billard reports tlie following case of sim- ple iinpcrforatidii of the anus. This child would doubtless have been sav-ed by the operation, had it not been for the gastro-eiiteritis. " Grenel, aged two days, entered by the Creche [the Jiatno given to the apartment, in which infants are depo- sited when Urst brought to the liospital] on the ninth of March. This child had passed no meconium since birth ; the abdomen was tumid and very painful, for the child cried and the fjice became pinched whenever the abdomen was touched. Tiie course of the colon could be felt through the parietes of the abdomen. He vomited green substances ; the cry was feeble ; skin cold ; and the circulation very slow. The anus was imperforate, although there existed the appearance of its orifice in the perimeum. I passed through a sharp-pointed bistoury, being careful to turn the back towards the bladder, and after having made the incision, I enlarged it in a back- ward direction. A large quantity of meconium immediately issued from the opening ; the swelling of the abdomen at once subsided, and the pains apparently ceased, for the child stopped crying, and the face no longer exhibited the expression of pain. He was immersed for half an hour in a bath of marshmallows ; but notwithstanding all these precautions, the vomiting continued, and he died at night. " The autopsy : On examining the body, a passive conges- tion of the pharj^nx was found, and on the mucous membrane of the stomach several patches of a vivid red, together with a universal redness and tumefaction of the inner membrane of the small intestines ; the muciparous follicles were very numerous in the large intestines ; the circumference of each of these follicles was surrounded by a red circle ; the rectum was continued to the perineeum, where it was only closed by a simple membrane. A large quantity of meconium \vas found in the laro^e intestines. The remainder of the intesti- nal tube contained some yellow adhesive matters. The cir- culatory and cerebral systems were healthy." {A Treatise on the Diseases of Infants. Stewart'^s English Version, p. 281. JS'ew York, 1839.) Cases XVIII. — XIX. — Mr. Ilowship reports the two following cases of simple imperforation of the anus. J^irst Case. — " S. P., a woman aged twenty-six years, was friglitened in the eighth month of her pregnancv, by a rat 6 ^ 82 THE SECOND SPECIES OF MALFOEMATIOX. leaping repeatedly at lier. Her alarm was considerable, but she recovered, and went her full time. In the birth the infant was observed to have a large belly. " On the second day after the child was born, the nurse observing there had been no appearance of stool, examined more particularly, and found there was no passage. The infant was therefore taken to a medical person in the neigh- borhood, who with a lancet divided the integument that cov- ered the end of the intestine. Meconium immediately appeared, and in due time faecal matter. " The evacuations from the bowels were always very thin, nearly black and extremely offensive. The discharge did not appear at intervals, as in common, but continually oozed out upon the napkins, showing there was no power of reten- tion in the parts. " In six months the child was again taken to the person who had punctured the intestine. The mother said that she was sure the passage was not sufficiently free. The surgeon, how- ever, was of a different opinion, insisted upon it, ' that every- thing was right,' and giving a powder for the infant, sent her away. " When the child was able to run alone, it was still neces- sary to keep a napkin constantly upon him. The stools passed without his knowledge, he was well enough aware of it afterwards, but although naturally a sharp boy, he never was conscious of it at the moment of its taking place. " His belly continued to enlarge, and when a year and a half old, it had formed a very large tumor, but unattended with any apparent inconvenience. The appetite was so excessive, that it amounted to a constant and unnatural crav- ing for food. He was perpetually observed to pick up, and eat whatever might be lying near him upon the ground, small l)its of stick or broom straws, plum, or fruit stones, etc. He seemed never to be satisfied, but would eat heartily, every hour through the day, nor did anything appear to disagree Nvirli him. " lie had been seen by several medical gentlemen, none of whom were satisfied as to the particular nature of his com- phiint. There was, indeed, a very large tumor in the abdo- men, but no sensation like tliat conveyed by a collection of water ; nor any hardness, or particular sensibility about the region of the liver, to warrant any suspicion of hepatic disease. " When two years old, the child was still suckling. The niotlier, from his peculiar state of health, considered he was not strono; enou2:h to be weaned. About this time he had THE SECOND SPECIES OF MALFORMATION, 83 haen out, and made some complaint of nneasiness and pain in his t)clly, and on roturrn'nr^ home, lay di>wn in the cradle, still nnea.sy. The i'ollowing (hay lie was worse, with a hot and dry skin, white tongue, thirst and extreme restlessness. Tiiere was now a constant and most distressing sense gf uneasiness in the helly. In the night he would creep to tlie edge of the cradle, and partly out, he would hang over, rest- ing his hands on the lloor, while the abdomen was pressed by the edge of the cradle. This posture appeared to give him partial relief." " Tlie i'ever and general irritation continued to increase daily to his death, Vv'hich took place six days subsequent to the commencement of the attack." " Post-Mortem Exammation. — The abdomen was exceed- ingly enlarged. On cutting into the cavity, a soft, white, elastic tumor was found. This tumor, traced by its connec- tions, proved to be the lower part of the intestine rectum. The stomach and small intestines were healthy, but the whole of the great intestine was enlarged to at least double its natural size. " Just where the rectum commences, the coats of the in- testine were suddenly expanded, forming a great oval pouch, or bag, sufficiently large to contain three pints of fluid. The structure of this bag was more dense and strong than that of tlie intestine in its natural state. " The contents of this bag were a very large quantity of fruit stones, with bits of stick, straws and dirt ; together with a large collected mass of fluid, dark fgecal matter, M-ith which the whole of the colon was more or less filled, as well as the large sac that contained the stones. " The enlargement of the rectum had extended itself quite down to the anus, so that to remove the tumor entire, it be- came necessary to dissect out part of the integuments which formed the artitical anus. The latter opening was found to be so confined, that it was with difficulty a bougie of middle size could be pushed through it. This opening consequently could give passage only to the thinnest kind of faacal matter." {Practical Ohservations in Surgery and Morhicl Anatomr/. p. 317. London: 1816.) Second Case. — " A medical friend, Dr. Samuel Merriman," says Mr. Howship, "to whom I mentioned the above case, acquainted me, that he had seen an instance, which he be- lieved to be of a very similar nature with the'preceeding one. A child was born with imperforate anus, and an enlarged abdomen. The integuments were punctured with a trocar, S4 THE SECOND SPECrES OF IVfALFDEl^rATION'. the meconium first appeared, and ftjecal matter subseqnentljr„ It was intended in this instance, to have formed an enhirged- and adequate orifice by the nse of bougies, or such other means as might liave been necessary ; bat the mother, botb ignorant and obstinate, was not to be prevailed upon to allow any thing more being done on tlie child's behalf- The infant went ott tolerably well for about six months, althouigh the- enlargement of the abdonaen continued to increase. He sub- sequently became poorly, and died. The body was not ex-^ amined." {Loe. cit. ;p. 320.) Cases XX. — XXI. — M, Di^areque records two cases- of this species of malformation upon which he operated. The first case was that of a child which had not passed meconium for thirty-six hours after birth. M. Bnpareque having acertained that there was imperforation of the anus,, opened it with great success. {Bevvoe Medicale de Paris. J/cn', 1835. jt?. 284.) M. Dupareque's second- case was a child to which he was- called in consultation, and wliich for thirty hours after Birtli had ])assed no meconium. M. Duparque having acertained that there was imperforation of the anus, succesfully per- formed the operation with a strait and narrow bistoury, A gum-elastie canula was placed in the rectum. Twelve or fifteen hours afterwards, all the signs of eflfu'sion of the ab- domen manifested themselves, and the child succumbed. At the autopsy the rectum was found to be softened and punc- tured at the point of union with the- sigmoid flexure of the colon. This accident was produced by the gmu-elastic canula, which from carelessness by the nurse had been too far ad- vanced, and kept too long in. {Loc. dt. jp. 285.) This case should be a warning to both surgeons and nurses- how they use canulas and bougies. In my opinion, the canula was by no means indicated in this instance, and should not have been used. Soft tents with the occasional use of the little finger were all that were i-equired to keep the passage patulous. Several cases in which similar accidents have occur- red from the careless manner of usiug canulas and bougies will be found recorded elsewhere in this work. Case XXIL — M. Petit reports, with several otliers, the case of a cliild presenting an imperforate anus, in which no sign of such an organ was visible. On the third day the THE SECOND SPECIES OF MALFORMATION, 85 mcinbrano elosini:; the anns, wliieli was both thick and firm, was incised by iiiin with a hanoet. The inecoiiium passed, but the child died in coiividsions. {Memoir-e deV AeademieJivyal/G U Clvirunjie de Paria. tome II. ]). 237. 1781.) Cask XXIII. — M. Petit m\ another occasion witnessed a new-born child which was destitute of an anus, or any sign of one- lie first attempted to incise the membrane which covered tlie anus, with a hmcet, but failed. He then empk)yed a trocar, when the meconium passed out freely ; nevertheless, the infant died on the ft^llowing day. {pj>. cit.) Cask XXIY.' — M. Saviard, Mdio was, at the time, chief •surgeon of the Hospital Hotel Dieu, in Paris, relates a case of simple occlusion of the annal orifice. " On the 16th of Kovember, 1693, an infant four days old was brought to tlie Hotel Dieu, whose anus was closed. Sa- viard examined the place where the natural aperture ought to have been, and perceived a membrane extended across" it, through which he could distinguish the meconium by its dark fiolor. He incised this membrane with a strait sharp-pointed bistoury, which afforded a passage to the contents of the bowels. After this he dressed the wound three days with a tent dipped in digestive to prevent its reunion, and the child was cured." {Nouveau Reoueil d^ Observations Chirurgicales. Ols.iri Park: 1702.) Case XXY. — The following account of a case of mon- strosity, having a closure of both ears, an imperforate anus, and a double fissure of the palate, was received from W, Otis Johnson, M. D., of Cambridge, Mass., and read to the Boston Society for Medical ImprovemeM, July 12th, 1858, by Jeffries Wyman, M. D., who also showed easts of the ears. " On the 16th of June, 185S, I was called early in the after- noon to Mrs. F., an intelligent woman, wife of a respectable zVmerican mechanic. In half an hour she was easily delivered of her third child. The first is living and is an unusually hand- some girl of about five years; the second died before the family came to Cambridge. Mrs, F, had previously told me that she had continued to nurse her second child three montlis ;after her last conception, which of course, there is reason to 4oubt, She considered her ' time ' as at hand. " The ' monster' gave no signs of life for more than a minute •f'cfter birth, and was what is professionally called hlue. The .coi'd was about the neck. In about tifteeu minutes after S6 THE SECOND SPECIES OF MALFORMATION. birth, having in the mean time made but a few faint cries, he gave out some half a dozen of the most unearthly shrieks for an infant I ever heard. These were repeated some eighteen hours afterwards. -' I found the ears closed and undeveloped^ as your casts will show ; a double fissure of the palate, and an imperforate anus. The ensemble of the features was idiotic ; the remain- ing development was perfect, and seemed to be that of a six months' or six and a half months' foetus. ''Thirty-six hours after birth, a fihn, of apparently mucous- membrane protruded from the anal fissure, and,, after reaching the size of about half an inch in diameter, burst, and meco- nium escaped. " The child continued to show an increasing vitality till about the thirtieth hour after birth, from which; time it began to sink, and died easily, forty -live hours after birth." {Records of the Boston Society for Medical Improvement, Vol. III. p. 214. Boston : 1859.) Case XXVI. — Ruysch saw a child whose anus was closed by a membrane. On the fifth day after its birth there was a spontaneous rupture of the occluding membrane and death soon followed. {Adversaria Anatomica, decad. II. Cajy. 10, p. 13.) Case XXYII. — Von Ammon reports the case of a male eliild in whom there existed an imperforation of the anus by a simple membrane which, he at once incised. In this instance there was quite a depression at tlie natural situation of the anus, and what was remarkable, the penis was in a constant state of priapism which continued until after the operation of incising the occluding membrane, and the complete evacuation of the rectum. This child was well formed in other respects and lived four months after the operation, the anus and the rectum perform- ing their functions admirably, the sphiuctores ani being- present and well formed. The child died of a scrofulous- diarrhoea. {D-le Angehorenen Ckirurgischen, KranTcTieiten Des Menschen, S. 4A. Berlin, 1S4:±) [Vide Plate. III.] The following authors have also seen and described cases of this peculiar species of malformation. Fabricius of Hildanus. {Ohsei^atiomtm Chirurrjicarum Genturia.. Cent. 1. Ohser. 73, p. 51. Basil^ 160G. Folia.)/ Fabricius ab Aquapendente. {0^. cit^- TUE SECOND SPECIES OF MALFOliMATIOX. 87 Villi Meeckrcn. [Olservationes Medico-Chirurgka. cap. XXIV. p. 114. Amstelod, 1G82. 8w.) Littre. {ITistoire de V Academic Royale des Sciences, annee 1710,^.47.) "Wagner. {Commer, Utierar. Xorimherg, p. 3G1, annee 1735.) Motais. {Mernoires de V Academic des Sciences., annee 1771, p. 5T9.) CT3:-A.P»TEIl IV. THE THIRD SPECIES OF MALFORMATIOIS. SECTION I. DESCRIPTION. Atresia Ani et Intestini Recti. In this si^ecies of arrested development the rectum does not descend as low in the pelvis as it should, but terminates abruptly in some form of cul-de- sac, at a variable distance above its natural outlet, and either hangs loosely in the pelvic cavity, or adheres to the anterior surface of the sacrum, or to the bladder, or to some contig- uous part. ISTo anus exists, and there is generally not even the trace of an anus to be observed in situ naturali^ the perinseal raphe being extended from the scrotum to the point of the coccyx without interruption. [ Yide Plate lY.,, Fig. 1.] The space which should, have been occupied by the anus and the absent portion of the inferior extremity of the rectum, is filled with some intermediate substance of a cellulo-fibrous nature. This is truly a deplorable form of congenital imperfection, especially should a considerable portion of the inferior extremity of the rectum be deficient ; then indeed the case becomes most serious and embarrassing to the surgeon, as there are no external signs by which he can ascertain posi- tively where the end of the rectum can be found, or, indeed, whether the organ even exists at all or not ; and to add fur- ther to the perplexity and the difficulty, the rectum, besides being abnormal, sometimes occupies an abnormal position. In all these respects, it will be observed that this species dif- TIIIO TIIIUI) SPECIES OF MALFORMATION. 89 fers most widely from the second species, in wliicli a swelling, a fluctuating tumor, or an accompanying projection or depres- sion in tlic natural situation of the anus, indicates the exist- ence and the position of the rectum, and directs the surgeon at once where to find it. From the nunihcr of cases of this species which are re- corded, and which I have presented, it might he inferred, that it is much more common than the first and second species ; but this would by no means be a rational conclusion, inasmuch as such cases scarcely ever escape notice, and are doubtless every one of them reported, both on account of their formidable, as well as their peculiar character. SECTION II. PHYSICAL EXPLOKATION— DIAGNOSIS. In these cases, in which there is no external indication whatever of either an anus or a rectum, it is of the utmost importance to success, that a minute and careful exploration should be made as a preliminary step to the treatment. The index finger of the right hand should be placed in the normal position of the anus, and pushed firmly np tow\^rds the pelvic cavity in the direction of the rectum, whilst, at the same time, with the left hand firm pressure upon the anterior walls of the abdomen, should be made, both inward and downward towards the finger in perinsieo. In this manner the ajjproach of the rectum towards the index finger, may be detected if it exists. Sometimes by the finger alone in the perinseum the fluctua- tion of the distended end of the rectum can be detected, should it not be too far distant. After having made an incision of the ]3roper depth in the di- 90 Tin: TllliU) SPECIKS OF ^[ALFOKMATIOX. rectiou of the rectiim, without discovering the end of it, the in- dex finger of one hand should be introduced to the bottom of the incision, whilst with the other hand, or the hands of an assistant placed upon the anterior walls of the abdomen, the intestines should be pressed down into the pelvic cavity. In this manner, if the rectum exists, it might be detected by the fino;er in the wound. . In these cases auscultation and percussion may also be used, in order to discover the presence or absence of the rectum. The stethoscope should be applied to the perinseum, and at the same time percussion should be made upon the walls of the abdomen. By these means the presence of the rectal exti*emity filled with gas and fsecal matter may be dis- covered. In arriving at a correct diagnosis in these obscure cases, con- siderable aid will be afi'orded by the introduction of the sound into the bladder, if possible, or into the vagina. Tlirough these media much may be discovered in relation to the exist- ence and the exact locality of the blind sac of the rectum. Mr. A. Copeland Hutchison recommends in these cases, gentle titillation of the skin with the finger, over the natural situation of the anus, which, he says, invariably causes the child to strain, or make efibrts to evacuate its bowels, and thereby produces a protrusion of this part, if the rectum is distended with meconium, which will be conspicuous, or felt in proportion to the contiguity of the intestine to the external surface ; unless indeed the rectum terminates quite high up, then there will be no protrusion whatever, and no fluctuation felt. {Oj>. cit, p. 269.) In some of the cases of congenital imperfection of the anus and the rectum, especially in the peculiar species under con- sideration, there is sometimes found a small excrescence or elevation of the skin in the form of a button, or of a crest, as will be observed in several of the cases I have reported. These excrescences, from their peculiar conformation, might at THE THIRD SPECIES OF MALFORMATIOX. 91 first sight, be regarded by a superficial observer as indicative of an anus, and also lead to the supposition that the rectum would be found in their immediate vicinity ; but sucli would not be the case, as they are altogether cutaneous in their structure, and liave no connection or communication wliatever with the blind end of the rectum which in these instances is generally quite remote from them. Sometimes a small dejjression or a pit, or a fissure or fissures of the skin exist at the place of the absent anus. Some exam- ples of this kind will also be found reported. SECTIOK III. PROGNOSIS. It has been a source of much regret that the treatment heretofore, of those cases, in which there is an absence of from one and a half, to two and a half inches of the inferior extremity of the rectum, has not been crowned with more suc- cess. "When, however, the serious and sometimes almost des- perate character of such cases is taken into consideration, as well as the many difliculties attending the old and imperfect methods of operating, the numerous failures heretofore, have nothing in them to cause surprise. One can well imagine the gravity of such an operation, and how difficult a thing it would be, even after having found and opened the end of the rectum, to establish permanently a canal in so soft and porous or spongy a substance as the peculiar tissue which in these cases fills the wliole space which the intestine itself should naturally occupy, and through which the artificial canal would necessarily have to pass, and how very inadequate such tissue would be as a substitute for the muscular rectum. The dilficultieSj therefore, enumerated by Bell, Yelpeau and 92 THE THIRD SPECIES OF MALFORMATION. others, of keejjing such a canal patulous, are by no means exaggerated or imaginary. These various considerations have induced many surgeons to look upon all such cases as entirely hopeless, considering the operation for their relief to be too grave and uncertain, and more hazardous and injurious than beneficial — hence they repudiate it altogether. Dr. J. H. Bigelow, Professor of Surgery in the Massachusetts Medical College of Harvard University, says that — " Judging from results, I do not consider the operation for imperforate rec- tum, or even for imperforate anus, a desirable one. I believe that in the present state of the art, it is better that a child born with either of these imperfections, should die without this operation ; although it must occasionally be performed in deference to established opinion." [Boston Medical and Sur- gical Journal, Vol. Z VII., p. 24:0. Boston: 1858.) I am surprised that so able a surgeon as Dr. Bigelow should have given this as his deliberate judgment ; that such doc- trine, so directly contrary to the genius of this age of real progress should have emanated from so high a source as the chair of surgery in the Medical Department of Old Harvard University. Should the sentiments of Dr. Bigelow be strictly and universally adopted, when, I ask him, would the " present * state of the art " arrive at that degree of j^erfection which would justify the operation ? Such views, if carried out to their le- gitimate consequences, would for ever close all the avenues to future improvement in the art, and be the burial ground of all further progress. Admit for the sake of argument, that the operation heretofore has utterly failed in every instance ; what then ? Are we on this account to abandon all such cases to their fate, in future ? Are we to sit down, fold our hands, quietly look on, and not make another earnest and in- telligent effort to save such ? Dr. Bigelow, however, says that this operation must occasionally be performed in defer- ence to established oj>inion. Can it be possible that Dr. Bige- low, through mere regard fjr established opinion would, Till': Tllliif) SI'ECIKS ()!•' MAi;i'"OKMATIUN. 93 imclor any circumstance, perfonii oi- :i(l\is(,' an ()})cratiou in which he had no conlidence whatever, and wliich he believed woiikl confer nothing, at best, but a lingering miserable deatli on the unfortunate little j^atient ? I admit that the results of the operation heretofore, have, in a majority of instances been unfortunate, but a much lai-ger number of cases have been saved by it, than is generally sup- posed ; and many of the fears of surgeons with regard to it, are ill founded and greatly exaggerated, as well as are their denunciations of it, unjust. Notwithstanding this proscription of the operation by several eminent surgeons, it is nevertheless sufficiently justified, even admitting the uncertainty and the danger attending it, by the success of a number of cases of a most desperate character, which wdll be found recorded in full in this chapter. The highly encouraging results in these cases, authorise and warrant an attempt at relief by some op- eration. An operation may not be followed by the desired re- sult, still an attempt should be made, unless there should be other complications or conditions of the system that would contra-indicate it. A very favorable issue, however, of the success of the operation in any of these cases must not be too confidently prognosticated. Some surgeons denounce the operation as being a cruel, a most barbarous proceeding, and on this account decline alto- gether to perform it. I would most respectfully refer all such to the reports of several cases given in this chapter, in which the little dying patients were so astonishingly relieved by the operation, that they immediately after nursed vigorously, slept most tranquilly, and ultimately recovered. The disrepute into which the treatment of such cases hereto- fore has fallen, may be in a great measure justly attributable to ignorance of the anatomical and pathological conditions and relations that pertain to these cases ; to the w^ant of skill in the operator ; to an imperfect method of operation ; to the operation being contra-indicated, &c. 94 THE TriTKD SPECIES OF MALFOR:\IATIO^*. Tlie treatment laid down and recommended in tliis chapter, if perse veringly carried out witli judgment, caution and tact, will, in my opinion, in the majority of cases, if not in all, not only preserve the life of the child, but also j)revent those sad consequences which so often unfortunately attended the treat- ment heretofore pursued. The celebrated French surgeons, MM. Amussat. Eoux de Brignoles and Goyraud, in their various publications on this subject, during the years 1834 and 1835, declared that pre- vious to that time, such cases as we are now considering, were never successfully treated, if treated at all, but were suflPered to perish, because, as they imagined, their predecessors had not sufficient skill and courage to make free incisions in the perinasum, in order to search for, and to find the blind end of the rectum, when it laid deep. Tliey claimed great merit to themselves for introducing as something entirely new in such cases, free incisions with a scalpel guided by the finger, instead of the old method of punctures with the lancet or the trocar. Although these gentlemen deserved great credit for calling public attention to this entirely neglected, but most important subject, at that time, and for introducing several valuable im- provements in the mode of operating, they nevertheless were egregiously mistaken in supposing that no bad cases of this kind were ever previously treated with success, and that they had the honor of first suggesting and putting into prac- tice the method by dissection with a scalpel guided by the finger. The evidence that will be adduced in this chapter will place this matter beyond all controversy. It will estab- lish the fact that such cases, even of the most desperate char- acter, Avere sometimes successfully treated both by dissection as well as by puncture, for years previous to the promulgation of the views of these gentlemen, and that they were by no means the originators of the method by dissection. Benjamin Bell more than half a century previous, not only taught, but successfully performed dissection in just such THE THIRD SPECIES OF MALFORMATK i.V. 95 cases. His directions for the performance of this operation, I will give in his own language. — " In such cases," says lie, " when the gut is found to lie deep, on the child heiug ])roperly secured, an incision of an inch in length should Itc made di- rectly on the spot where the anus ought to be ; and this should be continued by gradual and repeated strokes of the scalpel, in the direction the rectum is usually known to take ; not in a direct course through the axis of the pelvis ; for in that direction the vagina or bladder or perhaps both might be brought to sufter; but backwards and along the coccyx, wdiere there is no risk of w^ounding any part of importance. The best director in every case of this kind, is the finger of the operator. The fore finger of one hand being pushed in towards the coccyx, the surgeon with the scalpel in the other, should dissect gradually in this direction, either till he meets with fffices, or till the scalpel has reached at least the full length of his finger ; and if after all the feeces are not ' evacu- ated, as death must undoubtedly ensue if something further be not attempted, a long trocar should be pushed forward upon the finger in such a direction as the operator thinks will most probably meet with the gut." — (^1 System of Surgery. Vol. II. Ckaj). XIX. I). Ta. Edlnhurgh: 1787.) These were the graphic instructions of Mr. Bell, and he 'himself put them into successful execution in two formidable cases. [ Vide Cases XXX. — XXXI^ Tliis operation too was successfully performed in the year 1822, by the late and distinguished Mr. A. Copeland Hutchi- son, of England, whom I have already favorably noticed. The case upon wdiicli he operated w^as one among the worst on record, and the operation did not difter essentially from that recommended by Mr. Bell. I have reported the case in full. ■[ Vide Case XXXVI.^ A formidable case was successfully treated in the year 1800, now sixty years ago, in our own country, and in the then wilds of my owai adopted State — ^Iventucky. I feel proud to 96 THE THIRD SPECIES OF MALFORMATION. inform those distinguislied French snrgeons, that even at that distant day, and in the wild woods of Kentucky, a surgeon was found who possessed both the ability and the courage to execute successfully such a difficult and dangerous operation. Tluxt surgeon was Dr. John P. Campbell, of Flemingsburg, Kentucky. Tliis case of Dr. Campbell will be found reported in full. [ Vide Case XXXV.] SECTIOI^^ IV. THE TREATMENT. The treatment which holds out the greatest prospect of suc- cess in these cases, is that which contemplates the establish- ment of an artificial anus in the perinseum — Proctoplasty. By this operation the cul-de-sac of the rectum is sought for, through a passage made for this purpose by dissecting through the tissues which separate it from the cutaneous surface ; and when found of breaking up its adhesions, if any, seizing it with forceps, bringing it down, opening it, emptying its con- tents, and uniting its cut edges to those of the perinatal wound in the natural situation of the anus, according to the method of M. Amussat. If the blind sac of the rectum, how- ever, cannot be brought down without undue force, in conse- quence of the organ being too short, or its adhesions being too numerous and strong, it must be opened where it is, by a cnicial incision, and the passage which has been made to it, must be kept open and supply and perform the functions of that portion of the rectum which is wanting, according to the ordinary method. 1. When should the Operationhe Undertaken? Mr. A. Cope- land Hutchison advises in obscure cases of this character — that is, in cases in which it is very difficult to determine from Till'; THIRD SPKCIKS OK MALFORMATION. 97 present indications where the blind sue uf the rectum is, or whether this organ exists at all or not — to postpone the opera- tion, if possible, for twenty-four, or sixty hours after hirth, as no inconvenience will generally arise from the delay ; the dis- tention of the rectum by the meconium and fjiecal matter will be in the mean time, a most invaluable guide to the surgeon in making his incisions, and in searching for the cul-de-sac of the rectum. {Op, clt. p. 257.) Professor Dicffenbach recommends the operation to be per formed on the second day after the birth of the child, for the same reasons. {Die Operative Cldrurgie. Band 1. S. 672. Leipzig: 1845.) Although the delay advised by these authors is of much importance in facilitating the operation, and the search for the rectum, yet it is very liable to be abused, by being carried too far, for it is by no means as void of danger as they imagine. The primary object in such cases is to empty as soon as possible the distended intestines — lest they become inflamed, paralysed or lacerated, and thus jeopard the life of the child. When the operation has been delayed too long, the difficulty after its performance often is, that the bowels will not act at all, having completely lost their peristaltic ac- tion by having remained too long loaded and stretched with meconium and gas, and the child generally dies in a day or tw^o. I am of the opinion that the operation should be per- formed as soon as the child manifests its sufferings, by its cries or moans, and the agitation of its limbs, or its general restlessness ; or at least it ought not to be postponed longer than when free vomiting has taken place, because then the distention of the rectum by the meconium and the gas, which is so important in the search for the blind end of that organ, is sufficient for the purpose. The practice of administering purgatives for the purpose of forcing down the rectum, preparatory to the operation, cannot be too strongly reprobated. 7 98 THE THIKD SPECIES OF MALFOKMAIIOJT. 2. The Infant Pelvis. Some idea may be formed of the average dimensions of the infant pelvis in the normal state, by the' following admeasurements I made of it in two new-born, well-developed male infants, at full time : From one tuberosity of the ischium to the other — one inch and one line. From the os coccygis to the symphysis pubis — one inch and three lines. From the os coccygis to the jDromontory of the sacrum — one inch and two lines. From one tuberosity of the ischium to the other — one inch. From the os coccygis to the symjDhysis pubis — one inch and one and a half lines. From the os coccygis to the promontory of the sacrum — one inch and one line. In the instances in which the rectum is either partially or wholly absent, the pelvis is generally of smaller capacity than when normal, having also undergone to some extent an arrest of development, and being deformed to a greater or less degree. The tuberosities of the ischium approach nearer each other, in consecpience of the narrowness of the pelvic cavity common in these cases. Deej) incisions into the infant pelvis, are, as a matter of course, always attended with more or less difficulty and dan- ger. This of necessity must be so in such cases, on account of the small size of tlie pelvis as a theatre for such an opera- tion, especially when we take into consideration the presence of the important viscera which still further lessens its diame- ters, and the close proximity of the iliac and hypogastric arteries and veins which endanger the dissection in the search for the rectum. THE THIUD SPECIES OF MALFORMATION. 99 3. Introchtdioih of the Sound. Soinc surgeons, previous to performing the o^Jcration, recommend the introduction of a small silver sound or catheter into the bladder of the male, and a large metallic sound slightly curved, into the vagina of the female, to determine the direction and the position of tliese organs, in order to guard against wounding them. TJie first proceeding is difKcult and sometimes imj^ossible to accomplish, and neither of them, in my opinion, absolutely necessary, provided the oi^cration is cautiously conducted. 1 admit that the sound might considerably facilitate the searcli for the rectum along the anterior wall of the pelvis, whicli sometimes becomes necessary when the organ occupies an ab- normal position. 4. The Form of Incision. In the operation for perineal arti- ficial anus, surgeons have severally recommended the longitu- dinal.^ the transverse, the crucial, and the T incision. The longitudinal incision should, in my opinion, have the preference, because by it a larger wound may be obtained without danger, which sometimes becomes necessary in' mak- ing a thorough and extensive search for the rectal extremitv. This incision, if necessary, can be extended from the posterior margin of the scrotum, or from the posterior commissure of the labia majora, to the extremity of the coccyx. Another very important consideration is that by it, the cicatricial tis- sue which results from wounds in the vicinity of the anus is much less extensive than in any of the other incisions, and consequently greatly diminishes the risk of contraction after the operation. The transverse incision has no advantage whatever over the longitudinal, and should it be carried to the necessary extent, it might approach too near to the tuberosity of the ischium, and run the risk of wounding the internal pudic artery, and seriously injure also the sphincter ani muscles, as the pelvic cavity in these cases, is generally narrower, and the tuberosi- ties of the ischium much nearer each other than natural. 100 THE THIED SPECIES OF MALFORMATION. Tlie crucial and the T incision are botli objectionable on account of favoring the contraction of the anus by the formation of a greater extent of cicatricial tissue. Great care should be taken, that whatever incision is adopted, that it be healed by the first intention, as sup- puration always results in an increased extent of cicatricial tissue, and thus favors a greater contraction of the newly- formed anus. 5. The Sphinctores Ani Muscles. M. Eoux de Brignoles advises that' the perinseal artificial anus should always be established exactly in the mesial line of the sphincter ani mus- cles, and that in conducting the dissection, the fibres of these muscles should be most carefully separated, and their internal margin loosed, so as to preserve their freedom of action, and secure, what is of the greatest importance, their utility in the act of defecation. {Archives Generales de Medicine. 2d Ser. tome V. p. 475.) Tliis advice of M. Roux is highly important and judicious, and should, as far as practicable, be always followed, in all the cases in which those muscles do really exist. The task, however, of distinguishing and separating these muscular fibres, is by no means so easy to accomplish, as one would suppose from reading the remarks of M. Koux. M. Yelpeau says that this method of Eoux has no superior- ity over the ordinary one ; but this is a loose assertion of his, and does not merit much attention. Upon the subject of the invariable presence or absence of the sphinctores ani muscles in these particular cases of con- genital malformation, there is a singular diversity of opinion existing among authors. M. Eoux de Brignoles maintains that these muscles which receive their nutrient arteries from the ischiatic, are never wanting, that they exist independently of the rectum — ^lience his advice so to conduct the dissection, as to preserve them in TIIK Tllllil) SPECIES OF MALFORMATION. 101 connection with the iirtiticiul unus, luul thus euul)le the patient to have control over the retention of the fajces. {Memoire de VAcacUmie Iloyale de Medicine, tome 1 V. />. 183. Paris : 1835.) M. Bhindin, on tlie contrary however, asserts that when the anns is completely absent, he has ascertained that tlie sphincter muscle is invariably absent also ; this being always the case whether the skin does, or does not present an indica- tion of the natural situation of the anns — hence he advises that the artificial anus should be formed in the abdomen, because an artificial anus in the perinseuin, destitute of a sphincter muscle, would occasion incontinence of fseces to a greater ex- tent, and be attended witli more inconvenience and discom- fort, than one established in the abdomen. {Dictionnaire de Medicine et de Chirurgie Pratiques. Paris : 1832.) Tiingel, a late and very able German writer on abdominal artificial anus, considers the absence of the sphinctores and levatores ani muscles as a rule in congenital imperforation of the anus and the rectum ; and uses this as a strong argument against a perinoeal artificial anns, and in favor of an abdomi- nal one. ( Uher KunstlicJie Aflerbildung. S. 203. Kid : 1853.) M. Yelpeau is also of opinion that the sphincter muscle in all such cases is always absent. {OpeTati've Surgery. Vol. HI. p. 1090. Motfs English Versioii. New York : 1847.) M. Goyraud mentions it as an undeviating rule that the superior portion of the sphincter ani is always absent when the inferior portion of the rectum is deficient ; but that the inferior portion of this muscle, not only always exists, but is preternaturally developed in these cases — ^hence he comes to the same practical conclusions that M. Koux does. {Journal Ileldornadaire des Progress des Sciences et Institutions Medi- cales. tome III. p. 245. Paris : 1834.) M. Petit observes that in all such cases of imperforate anus, the sphincter ani muscle indeed exists, but it is so contracted, 102 THE THIKD SPECIES OF MALFOEMATION. ■wasted, and confounded with the surrounding parts, that it is difficult, or rather impossible for it to resume its function, with whatever care the operation may be performed. (Re- marques sur les differens vices de conformations que les enfans apportent en naissant. Mcmoire de V AcademieRoyale de Cliirurgie. tome II. Paris: 1781.) Mr. A. Copeland Hutchison mentions a case in which the sphinctores ani were wanting, but the levatores ani were per- fect and strong. {Op. cit. p. 271.) The only just and practical conclusions to be drawn from these conflicting opinions, are that, in some of these cases, the sphinctores ani muscles exist, whilst in others they do not ; but whether they are present or absent, the artificial anus should always, if possible, be established in the natural situa- tion in the perinseum, for should these muscles be absent, the infirmity is greatly less, even in this depending situation, than Blandin and Tiingel declare. Should these muscles, however, be present, the operation should be so especially conducted, as by all means to preserve their functions to the newly- formed anus as recommended by M. Eoux. I have elsewhere presented in full a highly interesting case successfully operated on by M. Roux. This case will com- pletely illustrate his peculiar and admirable method of ope- rating. \_Vide Case CLXYIIi\ 6. Abnormal Position of the Rectum. If the cul-de-sac of the rectum should not be found through the incision made \(^ the full extent in the normal direction and position of this in- testine, it is still no positive evidence that it does not exist, for as I have elsewhere already observed, that besides being abnormal, the rectum may sometimes occupy an abnormal position in the pelvic cavity — hence the important necessity of varying more or less the search for it before abandoning the case ; for continuing the search in the same direction would not only result in a failure to find it, but also, THK THIRD SPECIKS OF MALFOUMA.TION. Hl3 in tlie loss of the patient. Instances have occuiTcd in ■\vliicli the surgeon, after searching for the rectum in tlie natural direction and position of tliis organ, failed to find it there, and abandoned the case ; afterwards at the auto})sy he dis- covered it in another jjosition in the pelvic cavity, from which he might easily have drawn it into the incision he had made in the perinaeum, without any difficulty or danger, if during the operation this abnormal position of the rec- tum had been known or thought of. [ Vide Plate XI V. ] A number of cases will be found reported in this work, in which the discovery was made at the autopsy, that if the search for the end of the rectum had been varied even in a slight degree from the natural direction of this intestine, it would have been found, and the patient, in all probability, saved. Or if the point of the bistoury or trocar, in the opera- tion of puncture, had been slightly changed in its direction, the end of the rectum would have been penetrated. It is scarcely necessary to observe that during the oj^eration, the blood, from time to time, should be well sponged out of the wound, the haemorrhage, however, is generally but slight if proper care is taken ; and that the dissection should be con- ducted with as much dispatch as would be compatible with the safety of the child. Infants, however, are found, as I have elsewhere observed, to bear a great deal without any bad re- sults, provided no imj)ortant vessel or structure is injured. Y. The Method of Operating. When the operation is deter- mined on, the little patient should be placed on its back on a table, or on the lap of an assistant, as in the lateral operation for lithotomy, its legs should be flexed and held apart by two assistants, and the nates completely exposed and inclined for- ward. If the catheter or the sound is decided on being used, it must now be introduced and held by an assistant. The surgeon placing himself in front, should with the thumb and index finger of the left hand, stretch the integuments of the 104 THE THIRD SPECIES OF MALFORMATION. perineum, and with the round-bellied scalpel in his right, make a longitudinal incision on the median line through the skin, commencing with the posterior margin of the scrotum, or at the posterior j^oint of the commissure of the labia majora, and extending to the termination of the coccyx, unless he should think that a shorter incision would give him ample room. The lips of the wound now being drawn apart, the operator should dee23en the incision in the natural direction of the rectum, by cautiously incising little by little the different layers of the perinseum in succession as they present them- selves, exploring well with the index finger of the left hand before each stroke of the scalpel, to ascertain the position of the bladder or the vagina, so as* not to wound it, and also to recognize by the projection and the fluctuation, the blind sac of the rectum. Tlie finger is better than either the probe or the sound for this purpose, and it also serves to guide the knife, being the best, if not only director, that should be used in such cases. Extreme care should also be taken to avoid the great pelvic vessels at the sides, and the sacrum behind, lest as it regards the latter, the knife should get behind the rectum, of which it is in search, and miss it altogether, or wound it some distance above its cul-de-sac. After the opera- tor has penetrated as far as the pelvic aponeurosis without meeting the end of the rectum, he should then divide this tis- sue also, and search for it in the pelvic cavity. The edges of the wound may be kept asunder by crotchet hooks, so that the cavity may be explored both by touch and by sight. The finger can be introduced from two, to two and a half inches in depth, towards the promontory of the sacrum, so that the end of the rectum may be reached, if the organ is not enfirely wanting, or if it is not interrupted in its superior portion and adhering to the superior wall of the bladder. If in searching towards the promontory, of the sacrum, the rectum cannot be found, the operator should not fail to explore the anterior wall of the pelvis. To this end, the perinatal wound, if necessarv, TIIH TIIIKD SPECIES OF MALFOUMATION. 105 may be eiihir^xMl, in order to examine whether the tciiiiinul end of til e rectnni may not be adhering to the bladder, to llie vagina, or to the uterns. Should the operator at any time during the search detect with his finger a Huctuating tumor, more or less elastic, and of a dark-br(nvn color, which he can ascertain if necessary by the speculum ani, he may be assured that it is the rectum ; and when thoroughly convinced of this, he should seize the projecting end of it with the bull-dog forceps, or double tenaculum, and endeavor to draw it gently downwards into the perinteal wound ; no very considerable force, however, must be applied, and if it does not yield, it wdll be owing to adhesions which, if not too numerous and too strong, should be carefully loosened by the fingers, if possible, using the knife or scissors only when they are very firm, and rec^uire great care in their division. It is important and always very desirable that the projecting and terminal end of the rectum should be brought down into the perin^eal wound, but if this is impossible, in consequence of its locality and adhesions, the operator should not hesitate to seize any easy movable portion of the rectum which may be near, and bring it down into the external w^^und, to serve in the formation of the anus. The terminal end of the rectum being left in its position, and being cut off from the circulation of the f^cal matter, will gradually contract, and ultimately become obliterated. As soon as the end of the rectum is brought down suffi- ciently low, a needle armed with a double ligature should be passed through it, by means of which, and the forceps or hooks, it should be drawn down to the level of the integu- ments. The cul-de-sac should now be opened by a longitudi- nal incision from front to rear, its contents conq^letely emp- tied, the wound thoroughly cleansed, and its cut edges attached by six points of suture to the integument of the corresponding edges of the perinssal wound, in the exact and proper situation of the anus, care being taken that the mucous 106 THE THIKD SPECIES OF ilALFOEMATION. membrane should overlap the external skin, in order to pre- vent the stercoral matters from escaping into the cellular tis- sue between them. The remainder of the perinseal wound, both in front and behind the newly-formed anus, should then be closed by suture. The child's legs should be bound together by a bandage, the wound dressed with a compress dipped in a cooling lotion, and frequently renewed, over which the usual napkin should be applied to receive the dis- charges, and the child placed by the side of its mother in bed and kept warm. After the operation, it is indispensable to success that extreme care should be taken of the child. If the mother cannot nurse it, choice must be made of a good wet-nurse. Full baths and frequent emollient injections should be en- joined, and an equable temperature should be maintained in the apartment. The artificial opening, which always tends to contract, should also be closely watched, and sufficiently dilated, from time to time by the finger or elastic bougies. 8. Tlie Ordinary Method of Operating. By this method the end of the rectum is sought for, much in the same manner as by the preceding, but instead of being brought down when found, it is opened and suffered to remain in the exact posi- tion in w^hich it was discovered, and the passage which has been made up to it through the perinseum, must be kept open and supply that portion of the rectum which is absent. The difficulty and the success of this proceeding depend in a great measure upon the higher or the lower position of the blind sac of the rectum, for in proportion to the distance of the cul-de- sac from the skin of the perineum, will be the danger of faecal infiltration, and the difficulty of maintaining a sufficiently free and permanent opening after the operation. If the surgeon, after having found the cul-de-sac of the rec- tum, should find it impossible to bring it down into the perinseal wound as already advised, in consequence of its TIIK THIRD SPECIES OF aiALFORMATION. 107 peculiar position, its numerous and strong adiiesions, or its shortness, lie slioukl have recourse to the ordinary method. As soon as the rectum is discovered by the surgeon, its pro- jecting point should be well exposed, and the sharp-pointed bistoury, or a trocar, thrust into it, and the contents of the bowel evacuated, especial care being taken to make the punc- ture directly in the end, if possible, and not in the side of the rectum. The puncture thus made should then be enlarged crucially, with the probe-pointed bistoury guided by the lin- ger, taking care to make it sufficiently free and permanent at first, in order to avoid a second effort, as the tendency to con- traction is always much greater in subsequent operations. When the blind end of the rectum is thick, hard or knotty, resembling cicatricial tissue, as is sometimes the case, the whole of it, or as much of it as possible, should be removed, provided it can be done safely. After the opening has been sufficiently enlarged and the rectum completely emptied and washed out by warm mucilaginous enemata, that part of the perinseal wound, in front and rear of the portion designed for the anus, should now be closed by suture, taking care, how- ever, to leave a sufficiently ample opening, and in the proper place, for the new anus. A silver canula much in the form of a nipple, or similar to the tracheotomy tube, with a very slight curvature adapted to the direction of the rectum, the length of the newly-made passage, and about three-eighths of an inch in diameter, should now be introduced and secured in its situation by two strips of tape passed through rings at the external end of the canula, and tied in front and behind to a circular bandage fastened round the body. The usual napkin and a compress dipped in a cooling lotion, should now be applied, and the child put to bed. It would be advisable to have several of these tubes of dif- ferent sizes on hand, in order that while one was out and being cleansed, the other might be in. They should be con- structed with their superior extremity bevelled or rounded 108 THE TUIKD SPECIES OF MALFOKMATION. off, to facilitate tlieir introduction, and their inferior extremity should be furnished with a shoulder, anteriorly and poste- riorly, with a ring in each to put the tape through, for the purpose of confining them in their situation. [ Vide Plate 11, Figure 12.] The silver tubes are the best ; elastic ones, however, if lined with flexible metal, are very good and answer very well. Tlie canula should be frequently withdrawn and cleansed and the newly-made passage washed out, and should there exist any undue irritation, the parts should be often well bathed or fomented to allay it. The tube shields the raw and highly delicate surface of the newly-made canal from the irri- tating effects of the excretions, giving it, to some extent, that protection which a mucous surface affords ; it also, perhaps better than any other, preserves the continuity between the opened end of the rectum and the external parts, for the free passage of the faaces. The fulfilment of these indications is absolutely essential to the success of the operation. After the hollow instrument has been used for some time, or until complete cicatrization has taken place, it may be laid aside, and the finger, or the wax or elastic bougie occasionally passed, in order to preserve the passage patulous. 9. The Liability to Coarctation. To prevent coarctation or obliteration of the newly-formed canal, constitutes the most difficult, troublesome, and serious part of the after treatment of this, the ordinary method of operating, and a great obstacle to the success of the operation, especially in all instances in which the blind sac of the rectum has been found at consid- erable depth from the external surface. Mr. Benjamin Bell especially directs attention to this diflaculty in the two cases upon which he successfully operated. [ Vide Cases XXX— XXXI.^ Mr. Miller, of Methven, has recorded an interestinir case of this character, in which the tendency to the closure of the newly-formed opening was so great, that he was com- pelled to repeat the operation ten times before the little pa- THE THIRD SPKCIE3 OF MALFOKMATIOls'. lOO tient was eight mouths okL [Vide Case CXXXVII?\ An- other simihir and interesthig case is rehited by Mr. Francis McEvoy. \yid6 Case XXXI V?[ M. Velpeau says, '-The last portion of the intestine can never be reestablished but in a ver}^ imperfect manner. It is a listula which we substitute in place of the natural tube. The species of mucous surface which ultimately becomes developed, can but very feebly represent the tunics of the anus. Though the system be inca- pable of entirely closing up stercoral fistulas, it has a constant tendency to diminish them, so that they soon become nothing more than mere ducts for the passage of fluid matters. The absence of the sphincter, especially, is a fatal bar to success. When this is the case, it would be extremely probable that the anus w^hicli had been artificially reestablished would be one of the most difficult to keep open." {Op. cit. p. 1090.) Some surgical writers declare, however, that if the opera- tion is properly performed — that is, if the incisions are suffi- ciently extensive, no contraction or disposition to obliteration of the artificial canal will take place, and consequently no difficulty will be experienced in keeping it pervious. Among those authors may be named the celebrated French surgeon Dionis. {Cows d'' Operations de Chirurgie. Edit. IV. me. par La Faye. tome I. p. 391. Paris : 1740.) And also Mr. Malyn, a late English surgeon and writer, who says — '' Great stress is laid by some authorities on keeping a plug in the anus, to prevent the reunion of the sides of the wound. This misht be of some service if the incisions were so slight as only to serve for present exigencies ; as then the remainder of the cure must be effected by dilatation. But when the operation has been properly performed, there is no occasion for a plug, inasmuch as the cut having passed across the direction of the muscular fibres, they will retract and drag the faces of the incision away from each other, so that if the object were to reunite them, it would be most difficult to ac- complish." {Cyclopaedia of Practical Surgery. By W. B. 110 THE THIRD SPECIES OF MALFOEMATIOX. Costello, 2L D. Vol. I. Article^ AnxLS. p. 3-i3. London : 1841.) It appears to me, however, that such an operation as Mr. Malyn here recommends would completely destroy the power of the sphincter ani muscles, if they existed, and ever after occasion incontinence of faeces, an infirmity which might not be preferable to death. 10. The Objections of M. Amussat. Twenty-five years ago the celebrated JVI. Amussat, whose highly improved method, it will be observed, I have in part recommended and adopted, discarded the ordinary operation in these cases, in conse* quence of what he conceived to be the insurmountable difii- culties that always attend it. He declared most positively, that the ordinary method by simply incising down upon the rectum, when the blind sac of this organ laid deep, was en- tirely inefficient, and ultimately attended with uniform fail- ure. This he attempted to establish and maintain in a remarkably able paper, which was read before the Academy of Sciences on the second day of ]S"ovember, 1835, styled — " Histoire d'une Operation d? Anus artijiciel 2>'''':i'i^^ue cweo succes par un nouveau Precede^ dans un cas d^ Absence con- geniale de VAnus / suivie de quelqnes reflexions su?' les Obtu- rations du Rectum.'''' {Gazette Medicate de Paris. Ifovetn- bre 28, 1835.) It appears that M. Amussat was first led to reject the ordinary operation, from the circumstance of his having per- formed it unsuccessfully upon two cases, in each of which the rectum terminated between one and a half and two inches from the cutaneous surface of the perinseum. The operation, he says, was performed in the ordinary manner, by simply cutting down on the rectum, but both infants died jaundiced in a few days, which event he attributed to the absoi-ption of the bile and the meconium, consequent upon their coming in contact with a wound of such considerable extent. That M. THE THIRD SPECIES OF MALFOliMATION. Ill Aniussat, however, lias considerably exaggerated the imper- fections, difficulties and failures of the ordinary method, will be sufficiently obvious when we take into consideration the success which has attended it in numerous instances ; some of them, it will be observed, were of a most discouraging char- acter, the operation having been performed under the most unfavorable and embarrassing circumstances. lie has in thus imputing uniform failure heretofore to this operation, done injustice to the several able and distinguished surgeons who have in several instances performed it so successfully. The main objection that ]\^. Amussat urges against the op- eration, and the one which led him to reject it altogether, is, that the bile and the meconium are liable to be absorbed by the fresh surfaces of the wound made by the operation, and thus cause jaundice, or mortal degeneration of the blood. It was to this circumstance alone he attributed the loss of his two cases, already alluded to. M. Amussat, however, failed to verify this positive declaration of his, by 2^ jpost-mortem ex- amination of the biliary organs of his two unfortunate cases. I do not believe that the icteroid appearance of these cases had anything whatever to do with his operation — that this appearance of the skin was not caused by absorption of the bile and the meconium, in the manner he imagined. They doubtless would have died jaundiced had he not performed the operation, for it is a notorious fact that by far the largest number of such cases have this yellow tinge of the skin, inde- pendently of any operation. Nearly all such cases, unless completely relieved by the operation, die jaundiced ; the jaun- dice, however, is neither the result of the absorbtion of the bile and the meconium by the wound, nor is it the immediate cause of death. The operation, if timely and judiciously per- formed, instead of inducing jaundice, is the first step towards removing it, if it already exists, and of preventing it, if it does not exist. The icteroid tinge of the skin in these instances may be the result of the too long retention of the meconium 112 THE THIRD SPECIES OF MALFORMATION. in the intestines, or it may be tlie result of inflammation of tlie umbilical vein, or of the biliary ducts ; indeed, this icter- itious appearance is a phenomenon not unusual in infants of from two to three days old, even when no malformation at all exists, doubtless consequent upon a temporary excess of the colorino; matter of the bile in the serum of the blood, for I have myself often observed in the new-born the whole surface of the body, as well as the tunica conjunctiva, to acquire a yellow hue, more or less intense, the result of a slight or a severe acute hepatitis w^hich obstructs the circulation of the bile and causes its passage intq the blood. About one-third of all infants born, are more or less affected with icterus. The main objection of M. Amussat, to the ordinary operation uj^oii this ground has, therefore, in my opinion, no foundation in truth. His objections, however, to the operation, on account of the liability to closure of the newly made passage, to infil- tration and the formation of stercoral abscesses in the vicinity of the artificial anus, are much more plausible, for these acci- dents sometimes certainly occur, and they are serious obsta- cles to the success of the ordinary operation. 11. The Method of M. Amussat. The chief feature, or pecu- liarity of the method of M. Amussat, is the application to the anus of the principles and the practice which Dietfenbach ap- plies to the lips, in cases of narrowing and closure of the mouth. {Traits sur Vart de restaurer lea defformites de la face, par deplacement. Montpellier : 1842. Atlas.) I have already shown at the commencement of this section, that M Amussat advises the blind end of the rectum when found, to be detached from its adhesions for the purpose of bringing it down even with the external opening made by the incision, and there attaching its mucous membrane by sut- ures to the lips of skin formed by the edges of the cutaneous wound. It will thus be seen that the object of M. Amussat's method is to supply the whole track of the artificial canu'. TIIK TIIIKD SPECIES OF M^y.FORMATION. 113 with the luitunil tissues, wliich in these cases is the sreat desideratum, these tissues being already prepared and adapted to the exercise of" tlie functions Avliich tliey are designed, and will be called upon to perform. It must be admitted that M. Amussat's modification of tlie ordinary proceeding is in several respects a most decided and most admirable improvement — that it is highly ingenious and deservedly meritorous ; but it also must be admitted, how- ever, that it cannot be universally adopted ; that it is by no means void of danger, for by depressing the rectum too much, serious if not fatal consequences might be the result ; and that it is not, in every case, as essentially necessary'- to success as he intimates. It will doubtless succeed well in all cases in which the cul-de-sac of the rectum does not lie deep, and having no adhesions, floats loosely in the pelvic cavity, as it does in some instances ; or when it can easily be separated from its adhesions, or these themselves are capable of being stretched, so that it can be drawn down without much force or difficulty to its external position in the perinseum. It is however, on the contrary, impracticable when there is consid- erable deficiency of the rectum, the very cases in which it would be the most essential. The great difficulty in such cases is elongating the rectum sufficiently. In order, how- ever, to obviate this difficulty, M. Amussat advises that the artificial anus be established in the coccvofeal, instead of the perinEeal region, in as much as the blind end of the rectum, lying nearer the former than the latter, would consequently have a shorter distance to traverse in reaching the surface, by being drawn directly backward, than by being pulled downwards to the natural situation of the anus. He there- fore advises the external incision to be made immediately anterior to the coccyx, or to the left of this bone. He even advises the excision of the os coccygis, if necessary to gain room ; having himself on one occasion for this purpose, removed the extremity of this booe in a case of this kind. 8 Hi THE THIKD SPECIES OF MALFORMATION. The child, however, died a few days afterwards. [ Vide Case CXLIV.] It will be observed that M. Amussat, unlike M. Roux de Brignoles, in this respect, attaches no importance whatever to securing for the benefit of the artificial anns, the sphincter muscles, by bringing down the end of the rectum into imme- diate contact with them ; but on the contrary deprecates any attempt of the kind. For the purpose of making his favorite method sufhciently elastic to extend to all cases in which the end of the rectum can be reached, he would sacrifice both the natural situation of the anus, and the sphincter ani mus- cles. But to discard these invaluable adjuncts, on this •account merely, when they could be preserved by the ordi- nary method, or by that of M. Roux, would be a great error which should itself be discarded ; for without these it is impossible to establish the complete function of the artificial anus. The practice of M. Amussat, however, corresponds with his theory on this subject, which is that the interior outlet of the body is disposed in such a manner, indepen- dently of its muscular apparatus, as to favor voluntary reten- tion of the faeces ; consequently that the power of retaining and controling the discharge of the faeces does not solely depend, upon the sphincter muscles, for patients have been known to retain control over the alvine evacuations, after the excision of the inferior extremity of the rectum. He tliere- fore comes to the conclusion that the same power will exist after his operation for artificial anus in the coccygeal I'egion, and hence he imagines there is no necessity for the sphincter muscles. In this it will be seen he differs but little in opin- ion from Mr. O'Beirne. {JVew Views of the Process of Defe- cation. Dublin , 1833.) It was the dutv of M. Amussat, however, to have estab- lished his theory by undoubted facts, before drawing such conclusions from it. This he never did, and until he does, whether the operation is performed by the ordinar}-^ method. THE THIRD SPECIES OF MALFOUMATION. 115 or by Ills own, tlie iiutural Bituiitiuii ot" the uiius in the periii- seal region should be selected, and the sphincter muscles, if they exist, should always, if possible, be secured, so that the power of retaining the faeces by the artificial anus would without doubt fail to be preserved. The first case upon which M. Amerssat executed his inval- uable operation, was a very complicated and difficult one ; and as it is highly interesting and most fully illustrates his pecu- liar method, I have produced it entire. [ Vide Case XLII.\ 12. The Ojyeration of M. Amussat, performed hy others. Mr. Waters of Parsonstown, England, records a case of imperfor- ate anus and rectum, in which in 1.842 he performed a similar operation to that performed by M. Ainussat seven years pre- vious, (1835.) Complete success attended this operation. It is said that Mr. Waters was not at all aware of the method of M. Amussat when he performed this operation, but was led to adopt the plan he followed, solely by his own reflections upon the case. This may all be true, and it may afi'ord another example that good surgeons every where think alike and come to the same conclusions. One thing however is certain, that the operation of M. Amussat was notorious for seven years in France, previous to that performed by Mr. Wat- ers, and that the Channel only divided the two surgeons. I have presented Mr. Waters' case in full. [ Vide Case XLIII.] Mr. W. G. Smith of Vauxhall-Walk, London, in 1846, adopted in part the method of M. Amussat, in a very extra- ordinary case. Complete success was the result of the oper- ation. [^Vide Case XL IV.] Mr. West says that he was a witness to the great advanta- ges of M. Amussat's method in a little boy upon whom Mr. Shaw operated successfully a few years since at the Middle- sex Hospital. {Lectures on the Diseases of Infancy and Childhood. Led. XXXI. p. 377. Phil. 1854.) 110 THE THIKD SPECIES OF ISIALFORMATION. Dr. Hermann Friedberg, of Berlin, in a late and very able essay on Artiiicial Anus, higlilj extols the method of M- Amnssat, which he has more or less improved and faithfully carried out. He successfully operated on a grave and very interesting case by this method, somewhat modified by him- self, and as this case fully illustrates his method of operating, I have presented it in detail, translated from the French, having been unable to procure a German copy of his work. [Vide CaseXZVIL] Mr. Redfern Davies, of Birmingham, England, also highly approves of the method of M. Amussat, and proposes a modi- fication of it. His remarks on the subject are practical and certainly deserve attention. He did not, however, adopt his own suggestions in a case of imperforate anus and rectum upon which he operated. [ Vide Case Lll?^ The considera- tions, however, which influenced him not to do so in this case appear obvious enough. " The reasons," says he, " that induced me, at the time when the rectum was opened, to forgo even the attempt to bring it down were— that I deemed the distance, two and a quarter inches, at which it was situated from the external opening, to be so great as to preclude the possibility of so doing. Bound down as the rectum is by its foldof peritonseum, the meso-rectum, I feared to encounter the almost certain dangers of peritonitis, or pelvic cellulitis, which must inevitably be the probable consequence of the laceration of its connective tissues, to permit of its descent for such a distance. Besides, at such a depth, how great an uncertainty there must be as to what the forceps might seize hold of." And again, he says : — " With all due deference to the opinions of others, and in hopes that it will receive whatever of attention it may merit in their hands, I beg to lay before the opinion of my moi-e experienced professional brethren the following modification in the operative interference usually adopted in these cases, THE TIIIliD SPECIES OF MAI.FOKMATIOX. 117 wliicli T li;i(l intended, had the patient survived a sufficient length of time, to carry into clFect. As far as can be judged by the evidence of the published cases, death is the conse- quence of different causes, according as the rectum is, or is not, brought to the opening of the wound. If it is, death ensues from the injuries inflicted, by so doing. If it is not, death ensues, but secondarily, iu consequence of the difficulty to defecation being only partially removed. I would propose, therefore, to combine these two procedes, and endeavor to obtain, by extending the operative measures over a consider- able time, immunity from the evils of both : viz., supposing, in the first instance, that an opening had been made (as was done) into the rectum, nature being relieved, had not other influences intervened, the child would have lived pro tern. ; but then comes into consideration the subsequent difficulty in passing the stool, owing to a gradual narrowing of the passage. All this is said to be due to the mucous membrane not beiuo- continuous with the outlet. To remedy this, therefore, when the parts have recovered from the efiects of the first operation, introduce a pair of forceps, and, seizing hold of the lips of the opening into the rectum, endeavor to bring it down, not by one vigorous and decisive holding on by the forceps, and by main force bringing the gut to the external orifice, but by gently and repeatedly soliciting its descent, introducing the forceps at certain intervals, and gradually endeavoring to accomplish the end. If the rectum can be so moved from its position, and be brought lower down in the pelvis (and so by repeated attempts it has been proved) by one forcible extension, and even that sometimes crowned by success, how much more liively is it that success should attend the proceeding, when, by the almost imperceptible tractions made upon it, the great causes of failure, viz., peritonitis and pelvic cellulitis, would be removed, owing to the small amount of disturbance that lis THE THIRD SPECIES OF MALFORMATION. ■would take place in the soft parts. Although, as far as I am aware, this procede by successive stages has never before been broached in any writings on the subject, the idea was taken from a case reported in the " Lancet," vol. i. p. 493, 1S46, [ Vide, Case XLIY^ in which an incision was made into the perineum for a distance of three inches, and on the second day an attempt was made, by gently pulling, to draw down the gut, which was not, however, fastened to the external opening. One month afterwards the child was doing well. I am fully aware that there is a vast deal of essential diflference between this procede and the one I advocate : nevertheless, accomplishing the end by successive stages, is in this case shadowed out, and will, I trust, assume a definite status in surgery." {Ediiiburgh Medical Journal, March, 1S5S. m. XXXIILp. 811.) Although M. Amussat, in his very able and highly inter- esting and practical paper already alluded to, laid down his beautiful process for the establishment of an artificial anus in the perineeum, and demonstrated its practicability and com- plete success in the very first case upon which he executed it ; yet strange, passing strange, he never afterwards in other cases pursued this method to its consequences, but in place of it, adopted and practiced colotomy. He thus seemed to have designed and built a most beautiful superstructure, merely to gaze upon it for a moment, and then to demolish it. 13. The Operation hy Puncture. Perinseal puncture was the earliest method of operating in cases of congenital closure of the anus or the rectum, and is still recommended and per- formed by some surgeons of the present day. They use for this purpose a trocar, a pharyngotomus, a lancet, or some other piercing instrument, and thrusting it into theperinseum at the normal place of the anus, they make it follow the natural direction of the rectum with the intention of penetrat- ing the end of this intestine, should it be present and in its normal position. THE TIIIllD SPECIKS OF MALFOKMATION. 110 The metlioJ by puncture is recommended in consequence of its being very simple and quickly executed in urgent cases, even by tlie young and inexperienced surgeon. There are, however, but few cases on record in which this operation lias succeeded ; it should therefore be entirely abandoned at this day, with the exception of those cases in which the end of the rectum can be appreciated both by the sight and the touch — that is, in which it lies near the surface and is distended with gas and meconium, Tlie " hlind plunge''' of such an instrument into the perinteum in those cases in M'liich it is aboslutely requisite to penetrate deeply, is a most hazar- dous proceeding, and one well calculated to inflict fatal injury to some of the delicate and important organs of these parts. Such an instrument is exceedingly liable to perforate the bladder, especially as this organ, in cases in which there is considerable deficiency of the rectum, occupies a lai'ger space in the pelvis. There is indeed a great deal less cer- tainty in the result of this operation than perhaps in any other in surgery, "When the trocar or any instrument of the kind is used in these cases, the operator is compelled to follow the natural direction of the rectum, but, as I have shown elsewhere, this intestine often deviates from its normal course. Should the rectum be further in front or to either side than natural, it might be missed or not opened in its proper place, and the operation of course would fail, and the patient be lost ; whereas in the operation by dissection, the blind end of the rectum can be sought for, and if it exist, can be found somewhere in the pelvic cavity within the safe limits of the operation. Of all other openings too, those made by puncture are the most liable to contract and become obliterated. Puncture therefore, in my opinion, can never be substituted for dissection in these cases, without great uncertainty, risk and danger. M. Petit, when speaking of the operation by puncture, ob- serves that it is very difficult to find the right place for 120 THE THIKD SPECIES OF MALFOKMATIOIS". inakiiii? the perforation into the blind end of the rectum, as he o-enerally found it formed into a knot in these cases. For performing such an operation, he recommends a trocar, the canuhi and circuhir phite of which are so slit open, as to serve as a groove for a lancet or bistoury to run in, to enlarge the aperture, after the trocar has been pushed into the blind end of the rectum. {Memoire de VAoadmnie BoyaleldeChirurgie. tome I.) Wolf mentions a very bad case of imperforation of the anus and rectum, in which he used the pharyngotome with complete success. [ Vide Case LIX.I Yon Schleiss, of Munich, reports a highly interesting case of imperforation or absence of the rectum, above a normal anus, in which he succeeded admirably by the happy phmge of a trocar. [ Vide Case XC] Dr. James Jones, of New Orleans, Professor of tlie Practice of Medicine in the Medical Department of the University of Louisiana, and a co-editor of the Kew" Orleans Medical and Surgical Journal, reports three interesting cases of imperfora- tion of the anus and rectum, in which the operation by punc- ture M'as performed with apparent success, but unfortunately these cases terminated fatally in a short time after the opera- tion. [ Vide Cases ZX, LXL, LXXX VIII.'\ 14. Modification of the Operation l>y Puncture. The late able and distinguished surgeon, A. Copeland Hutchison, whom I have already several times quoted, proposes a modification of the operation by puncture. His method is to use the trocar after iiaving made an incision in the ordinary manner with the scalpel a certain depth without finding the rectum. He says — " After having cut to the depth of about an inch and a half with the scalpel, which will be as deep as can be done with safety with tin's instrument, and there is no appearance of meconium ; we should then lay aside the scalpel and recommend the introduction of the point of a middle-sized THE THIRD SPECIES OF MALFOKMATION, 121 common trocar to the l)ottom of such incision. This instrn- ment should then he puslied gently upwards and hackwards, inclining rather to the left of the hollow of the sacrum and natural descent of the rectum, as far as the surgeon lliinks it prudcMit, or nnlil he imagines, from a want of resistance to the force employed, that he has penetrated the gut." {Oj). cit. p. 2(jO.) It will he perceived that the process of Mr, Hutchison does not differ very essentially from the ordinary operation by dis- section, and hut little from that of Benjamin Bell; consisting mainly in this — that he considers it too unsafe to carry the incisions with the scalpel heyond one inch and a half, and that from this point the trocar is the best and safest instru- ment. He operated successfully on a case of imperforation of the anus and rectum, Mdiicli I have given entire, and which will illustrate his method of operating, and prove highly interesting on account of the great depth which had to be cut through, before the blind end of the rectum was penetrated. [ Vide Case XXXVI.] Dieffenbach has also modified the operation by puncture. He coiftmences the operation in the perinseum by a small crucial incision, excises the flaps to make more room, and continues the depth of the crucial incision, esj)ecially the lon- gitudinal one, directing it graduall}'- backwards until he reaches one inch in depth. If no evacuation of fsecal matter takes place, he then lays aside the bistoury for a small trocar, and making a firm compression of the abdomen, pushes the instrument upward and backward from the bottom of the wound, following the concavity of the sacrum for a depth of an inch and a half to two inches. After the stilette is with- drawn from the canula, he introduces a large solid silver sound, and endeavors by this means to reach the cavity of the pelvis. When by plunging the stilette yet further, a measure which he regards as very hazardous, he does not reach the rectum, he withdraws the canula, introduces into the canal a 122 TIIE THIRD SPECIES OF MALFORMATION, piece of soft sponge, and postpones the rest of the operation to the next day. If notwithstanding the distention jjroduced hj the sponge, lie perceives no intestinal extremity in motion, from the pressure of faecal matter which fills it, he closes the wound with pieces of adhesive plaster, and has recourse to colotomy. But if the sound penetrates into a cavity, and is easily introduced for some distance, and if a little meconium flows, he proceeds to enlarge the wound. In order not to lose the opening, he withdraws the canula upon the sound, which he leaves in place, introduces by its side a large grooved director, withdraws the solid sound, places the director in the hands of an assistant, and following the groove, introduces into the rectum a strait blunt-pointed bistoury and enlarges on four sides the wound made with the trocar. When at last the opening is sufficiently large to allow a perfectly free passage, he injects with tepid water, by means of a short elastic canula, evacuates the bowel as thoroughly as possible, and then by means of the sound inserts a pledget of lint besmeared with cerate. If it is possible, he brings down the opened end of the rectum, and unites it to the edges of the wound in the skin. {Die Operative Chirurgie. Band. I. S. 673. Lei2)zig : 1845.) 15. Failure to foi^n a Perinceal Artificial Anus. Should the surgeon, in consequence of the absence or the great dejDth of the rectum, fail to reach it, and consequently fail to establish an artificial anus in the perinseal region by the directions and improved method I have already presented for this purpose ; or should the case be of such a character, that these measures, or the ordinary operation would be considered altogether im- practicable, he should then proceed at once to form an artifi- cial anus in the abdomen. This operation, however, should never be performed but upon the most mature reflection, after having made a most minute and careful examination of the case, and from a firm conviction that it offers the only THE THIRD SPECIES OF MALFORMATION. 123 terms upon ■which tlie life of the little patient can he pnr- cliased. [ Vide the chapter on ^^ Abdominal ArtlJiQial Anus.''^^ SECTION V. CASES AND REMARKS. Case XXVIII. — M. Fenerly reports the following very in- teresting case of imperforate anus and rectum :' " On "the 30th of March, 1857, a male child was brought to M. Archigene, born at full time twenty-live hours previously. The child appeared well developed and healthy. The parents as well as the midwife did not perceive at first the malforma- tion which caused them to call him in. It was not till eighteen hours after birth, and when the child began to toss about and cry, that the parents discovered the absence of the anal opening. " At the hrst visit the symptoms were as follows : The child was very restless, cried violently, and refused the breast. The respiration at first normal, soon became short and laborious, ;he skin was blueish, the abdomen swollen and painfully dis- tended ; the child seemed to suffer excruciatingly wdth colic. " On examination of the perinfeum there appeared no mark or vestige of an anal opening. Tlie raphe existed very clearly ; it commenced at the inferior extremity of the coccyx, and continued into the perinseal region ; the skin presented no change of structure. No depression existed at a point cor- responding with the anal orifice ; only when the child made efibrts to cry, a slight elevation was perceived. " The scrotum contained but one testicle, the right one was still retained within the ring ; the child had already urinated several times. "Tlie imperforation being quite evident, M. Archigene and M. Fenerly proceeded to the operation. After having placed the child upon the table, the legs flexed and separated, M. Fenerly explored the perinaeal region, and precisely on the spot which raised up, during an eflort, he made an incision. He first divided the skin to the extent of about one inch, then the underlayers in succession to the depth of five-eighths of an inch, taking care to direct the bistoury, at first perpendic- ularly, then inclining it gradually towards the sacrum, so as 124 THE THIRD SPECIES OF MALFOEMATIOiq^. to avoid the bladder, and following the usual course of the sacrum. The fore-finger which directed the bistoury, at the same time that it explored the depth of the wound, felt now a fluctuating point ; into this the bistoury was plunged, and immediately a large quantity of meconium issued. Ihe child was at once relieved, the respiration became normal, and the abdomen decreased in size. After having evacuated the intes- tine and washed out the rectum, he introduced an elastic sound smeared with cerate. The child sucked vigorously and slept perfectly well. The third day after the operation, MM. Fenerly and Archigene saw the child again. The blueish color of the skin had disappeared ; the evacuations were nor- mal, yellow in color and more moderate in quantity ; the general health of the child was good. They continued to intro- duce an elastic sound of large caliber. " On the twelfth day after the operation the child was well ; the wound completely cicatrized without contraction. The little patient now has an anus whose opening is nearly five- eighths of an inch in size." {Gazette des Hojntaux de Paris. Aunee 1857. A?>. XCVIII. p. 391. From Gazette Medi- cate d^ Orient.) Case XXIX. — The following very interesting case is re- ported by Dr. A. B. Shipman, of Cortland ville, X. Y., in a letter to the editor of the " Boston Medical and Surgical Journal,^'' dated October, 18i0. " On the 30th of October, 1838, Elizur Graves, of Solon, in this county, consulted me respecting a child of his, ^t. three months, for a malformation of the anus, which was congenital. It was not discovered until some days after birth, when, after repeated exhibition of cathartic medicines, no evacuation taking place, the nurse, on attempting to exhibit an enema, found no opening. A practitioner Avas consulted, who gave ► an unfavorable prognosis as to any remedy, and the child was considered as among the incurable. But as it continued to live, and even to tlu-ive, at the end of three months the parents brought it to me. On examination, there was no opening into the rectum, but a little posterior to the natural situation of the anus a slight projection of the skin was observed, which, on examination, gave an obscure feel of fluctuation. Tlie skin was also slightly inflamed. I advised an opening into this point, which the parents readily assented to, and it was accor- dingly made, and about a tablespoonful of pus discharged, but no faeces as was expected. I next examined the opening with a probe, but could find no communication w,ith the bowel. I next passed a sharp-pointed narrow bistoury, with the edge TIIK TIIIKD SPECIES OF ^fALFOltMATION. i25 towards tlic yacnim, in tliu diiveti(jii oi" lliu ivctuiii, the dis- tance of tlirce Indies. It was witlidrawn, and the ])oint found smeared with foeces. Considerable luiiinorrhage followed. I next introducep. cit. ]). 278.) Cases XXXII — XXXIII. — Latta mentions two cases of this species of malformation, in which he operated \vith complete success. He says he found it necessary in both these cases to make an incision of one inch and a half in depth before the rectum could be laid fully open, so as to allow free exit for the faeces. Oval canuljB were introduced and removed once every twenty-four hours. In two months there was a cure. The instrument, however, was used for nine months, to pre- vent contraction. {A Practical System of Surgery. Vol.11, p. 8T. Edhiburgh : 1795.) Case XXXIV. — Mr. Francis McEvoy reports the following case in a letter to the Editor of the " London Lancet,''' dated Balbriggan Dispensary, October, 1846. "Sir, — My father, who held the same medical office in this dispensary as I now hold, was requested to see an infant, whom he found with imperforate anus. There was no indica- tion whatever of an opening, no discoloration or elevation, but the skin was quite natural. The child was twenty hours old, and had had several convulsive lits, and three or four doses of castor oil, and some warm baths had been adminis- tered. Before discovering the imperfection which my father THE TniRD SPECIES OF MALFORMATION. 127 was cdlcMl to treat, an openiiifv was nia